A human mitochondrial poly(A) polymerase mutation reveals the complexities of post-transcriptional mitochondrial gene expression.
about
Identification of LACTB2, a metallo-β-lactamase protein, as a human mitochondrial endoribonucleaseEnergizing Genetics and Epi-genetics: Role in the Regulation of Mitochondrial Function.SLIRP Regulates the Rate of Mitochondrial Protein Synthesis and Protects LRPPRC from Degradation.Mitochondrial transcript maturation and its disordersSUV3 helicase is required for correct processing of mitochondrial transcripts.Mitochondrial Polyadenylation Is a One-Step Process Required for mRNA Integrity and tRNA Maturation.LRPPRC mutations cause early-onset multisystem mitochondrial disease outside of the French-Canadian population.SLIRP stabilizes LRPPRC via an RRM-PPR protein interface.Systematic review of autosomal recessive ataxias and proposal for a classification.The Pseudouridine Synthase RPUSD4 Is an Essential Component of Mitochondrial RNA GranulesHuman mitochondrial ribosomes can switch structural tRNAs - but when and why?Maturation of selected human mitochondrial tRNAs requires deadenylation.The process of mammalian mitochondrial protein synthesis.Mitochondrial RNA granules: Compartmentalizing mitochondrial gene expressionHuman mitochondrial nucleases.Regulation of Mammalian Mitochondrial Gene Expression: Recent Advances.Structure of mitochondrial poly(A) RNA polymerase reveals the structural basis for dimerization, ATP selectivity and the SPAX4 disease phenotype.Transcription profiling suggests that mitochondrial topoisomerase IB acts as a topological barrier and regulator of mitochondrial DNA transcription.LRPPRC-mediated folding of the mitochondrial transcriptome.Biochemical and structural bioinformatics studies of fungal CutA nucleotidyltransferases explain their unusual specificity toward CTP and increased tendency for cytidine incorporation at the 3'-terminal positions of synthesized tails.Polyadenylation and degradation of structurally abnormal mitochondrial tRNAs in human cells.
P2860
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P2860
A human mitochondrial poly(A) polymerase mutation reveals the complexities of post-transcriptional mitochondrial gene expression.
description
2014 nî lūn-bûn
@nan
2014 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2014 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
2014年の論文
@ja
2014年論文
@yue
2014年論文
@zh-hant
2014年論文
@zh-hk
2014年論文
@zh-mo
2014年論文
@zh-tw
2014年论文
@wuu
name
A human mitochondrial poly
@nl
A human mitochondrial poly(A) ...... mitochondrial gene expression.
@ast
A human mitochondrial poly(A) ...... mitochondrial gene expression.
@en
type
label
A human mitochondrial poly
@nl
A human mitochondrial poly(A) ...... mitochondrial gene expression.
@ast
A human mitochondrial poly(A) ...... mitochondrial gene expression.
@en
prefLabel
A human mitochondrial poly
@nl
A human mitochondrial poly(A) ...... mitochondrial gene expression.
@ast
A human mitochondrial poly(A) ...... mitochondrial gene expression.
@en
P2093
P2860
P50
P356
P1476
A human mitochondrial poly(A) ...... mitochondrial gene expression
@en
P2093
Alexis A Jourdain
Andrew H Crosby
Arnaud Baslé
Harold E Cross
Henrik Spåhr
Hue-Tran Hornig-Do
Jeong Ho Chang
Lorraine Hewitt
Maria Falkenberg
Nils-Göran Larsson
P2860
P304
P356
10.1093/HMG/DDU352
P577
2014-07-09T00:00:00Z