The human peroxisomal ABC half transporter ALDP functions as a homodimer and accepts acyl-CoA esters
about
The role of ELOVL1 in very long-chain fatty acid homeostasis and X-linked adrenoleukodystrophyHow to move an amphipathic molecule across a lipid bilayer: different mechanisms for different ABC transporters?Peroxisomes in brain development and functionPeroxisomal ABC transporters: functions and mechanismThe genetic landscape of X-linked adrenoleukodystrophy: inheritance, mutations, modifier genes, and diagnosisABC Transporter Subfamily D: Distinct Differences in Behavior between ABCD1-3 and ABCD4 in Subcellular Localization, Function, and Human DiseaseX-linked adrenoleukodystrophy (X-ALD): clinical presentation and guidelines for diagnosis, follow-up and management.The Concise Guide to PHARMACOLOGY 2013/14: transporters.Oxidative stress and adrenocortical insufficiency.Genome-wide identification and evolution of ATP-binding cassette transporters in the ciliate Tetrahymena thermophila: A case of functional divergence in a multigene familyApplication of a diagnostic methodology by quantification of 26:0 lysophosphatidylcholine in dried blood spots for Japanese newborn screening of X-linked adrenoleukodystrophyFatty acid omega-oxidation as a rescue pathway for fatty acid oxidation disorders in humans.Barley has two peroxisomal ABC transporters with multiple functions in β-oxidationStructure-function analysis of peroxisomal ATP-binding cassette transporters using chimeric dimers.CD1 gene polymorphisms and phenotypic variability in X-linked adrenoleukodystrophy.Drug resistance is conferred on the model yeast Saccharomyces cerevisiae by expression of full-length melanoma-associated human ATP-binding cassette transporter ABCB5.Pathophysiology of X-linked adrenoleukodystrophy.Metabolism of very long-chain Fatty acids: genes and pathophysiology.Pathomechanisms underlying X-adrenoleukodystrophy: a three-hit hypothesis.X-linked adrenoleukodystrophy: molecular and functional analysis of the ABCD1 gene in Argentinean patientsABCD2 is a direct target of β-catenin and TCF-4: implications for X-linked adrenoleukodystrophy therapyAntioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.Autophagy induction halts axonal degeneration in a mouse model of X-adrenoleukodystrophy.Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy.Involvement of the carboxyl-terminal region of the yeast peroxisomal half ABC transporter Pxa2p in its interaction with Pxa1p and in transporter function.ABCD1 deletion-induced mitochondrial dysfunction is corrected by SAHA: implication for adrenoleukodystrophy.Mammalian peroxisomal ABC transporters: from endogenous substrates to pathology and clinical significance.Functional genomic analysis unravels a metabolic-inflammatory interplay in adrenoleukodystrophyDiscovery of regulatory elements in human ATP-binding cassette transporters through expression quantitative trait mapping.The absence of ABCD2 sensitizes mice to disruptions in lipid metabolism by dietary erucic acid.Adrenoleukodystrophy: a forgotten diagnosis in children with primary Addison's diseasePioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophyPeroxisomal acyl-CoA synthetasesOxidative stress modulates mitochondrial failure and cyclophilin D function in X-linked adrenoleukodystrophyIntrinsic acyl-CoA thioesterase activity of a peroxisomal ATP binding cassette transporter is required for transport and metabolism of fatty acidsImpaired very long-chain acyl-CoA β-oxidation in human X-linked adrenoleukodystrophy fibroblasts is a direct consequence of ABCD1 transporter dysfunction.Mutations in the Arabidopsis peroxisomal ABC transporter COMATOSE allow differentiation between multiple functions in planta: insights from an allelic series.A Novel Double Mutation in the ABCD1 Gene in a Patient with X-linked Adrenoleukodystrophy: Analysis of the Stability and Function of the Mutant ABCD1 Protein.Mitochondrial ABC transporters function: the role of ABCB10 (ABC-me) as a novel player in cellular handling of reactive oxygen species.The significance of peroxisome function in chronological aging of Saccharomyces cerevisiae.
P2860
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P248
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P2860
The human peroxisomal ABC half transporter ALDP functions as a homodimer and accepts acyl-CoA esters
description
2008 nî lūn-bûn
@nan
2008 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
name
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@ast
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@en
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@en-gb
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@nl
type
label
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@ast
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@en
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@en-gb
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@nl
prefLabel
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@ast
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@en
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@en-gb
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@nl
P2093
P3181
P356
P1433
P1476
The human peroxisomal ABC half ...... er and accepts acyl-CoA esters
@en
P2093
Arno van Cruchten
Carlo W T van Roermund
Hans R Waterham
Lodewijk Ijlst
Maxim Boek
Wouter F Visser
P304
P3181
P356
10.1096/FJ.08-110866
P407
P577
2008-12-01T00:00:00Z