Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy. - Test2 - elhamkhani - TriplyDB

Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy.

Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy.

http://www.wikidata.org/entity/Q35193956

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Functional Characterization of IPSC-Derived Brain Cells as a Model for X-Linked Adrenoleukodystrophy Oxidative stress and adrenocortical insufficiency.Methylene blue upregulates Nrf2/ARE genes and prevents tau-related neurotoxicity Abcd2 is a strong modifier of the metabolic impairments in peritoneal macrophages of ABCD1-deficient mice Autophagy induction halts axonal degeneration in a mouse model of X-adrenoleukodystrophy.ABCD1 deletion-induced mitochondrial dysfunction is corrected by SAHA: implication for adrenoleukodystrophy.Functional genomic analysis unravels a metabolic-inflammatory interplay in adrenoleukodystrophy Pioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophy Partial rescue of Rett syndrome by ω-3 polyunsaturated fatty acids (PUFAs) oil Induction of mitochondrial changes associated with oxidative stress on very long chain fatty acids (C22:0, C24:0, or C26:0)-treated human neuronal cells (SK-NB-E).Activation of sirtuin 1 as therapy for the peroxisomal disease adrenoleukodystrophy.Oxidative stress modulates mitochondrial failure and cyclophilin D function in X-linked adrenoleukodystrophy Glutathione imbalance in patients with X-linked adrenoleukodystrophy Tauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy.The peroxisome: an update on mysteries.Mitochondrial dysfunction in central nervous system white matter disorders.X-linked adrenoleukodystrophy: pathogenesis and treatment.Peroxisome-mitochondria interplay and disease.Peroxisomal Disorders: A Review on Cerebellar Pathologies.Mechanisms of Antioxidant Induction with High-Dose N-Acetylcysteine in Childhood Cerebral Adrenoleukodystrophy.Evidence of Oxidative Stress and Secondary Mitochondrial Dysfunction in Metabolic and Non-Metabolic Disorders.Peroxisome deficiency but not the defect in ether lipid synthesis causes activation of the innate immune system and axonal loss in the central nervous system Combined mineralocorticoid and glucocorticoid deficiency is caused by a novel founder nicotinamide nucleotide transhydrogenase mutation that alters mitochondrial morphology and increases oxidative stress.Oxidative stress and mitochondrial dynamics malfunction are linked in Pelizaeus-Merzbacher disease.Cyclophilin D: a therapeutic target to counteract reactive oxygen species-mediated damage in neurodegenerative disease?The effect of the ALAnerv nutritional supplement on some oxidative stress markers in postacute stroke patients undergoing rehabilitation.Impaired mitochondrial oxidative phosphorylation in the peroxisomal disease X-linked adrenoleukodystrophy.Leukodystrophy: Basic and Clinical.

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Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy.

http://www.wikidata.org/entity/Q35193956

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2011 nî lūn-bûn

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2011 թուականի Յունիսին հրատարակուած գիտական յօդուած

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2011年の論文

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2011年論文

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2011年論文

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2011年论文

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Oxidative damage compromises e ...... del of X-adrenoleukodystrophy.

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Antioxidants & Redox Signaling

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P2860

The human peroxisomal ABC half transporter ALDP functions as a homodimer and accepts acyl-CoA esters

Parkinson phenotype in aged PINK1-deficient mice is accompanied by progressive mitochondrial dysfunction in absence of neurodegeneration.

Mitochondrial dysfunction and oxidative stress in neurodegenerative diseases

Beneficial effects of creatine, CoQ10, and lipoic acid in mitochondrial disorders

Mitochondrial alterations caused by defective peroxisomal biogenesis in a mouse model for Zellweger syndrome (PEX5 knockout mouse)

Cellular stress responses, the hormesis paradigm, and vitagenes: novel targets for therapeutic intervention in neurodegenerative disorders

Redox-dependent modulation of aconitase activity in intact mitochondria

Accumulation of DNA damage and reduced levels of nicotine adenine dinucleotide in the brains of Atm-deficient mice

Diabetic beta-cells can achieve self-protection against oxidative stress through an adaptive up-regulation of their antioxidant defenses.

Alpha-ketoglutarate dehydrogenase: a target and generator of oxidative stress

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