Disruption of a mitochondrial RNA-binding protein gene results in decreased cytochrome b expression and a marked reduction in ubiquinol-cytochrome c reductase activity in mouse heart mitochondria
about
LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAsC7orf30 is necessary for biogenesis of the large subunit of the mitochondrial ribosomePentatricopeptide repeat domain protein 3 associates with the mitochondrial small ribosomal subunit and regulates translationPentatricopeptide repeat domain protein 1 lowers the levels of mitochondrial leucine tRNAs in cellsThe human mitochondrial transcriptome and the RNA-binding proteins that regulate its expressionMitochondrial ribonuclease P structure provides insight into the evolution of catalytic strategies for precursor-tRNA 5' processingA computational screen for regulators of oxidative phosphorylation implicates SLIRP in mitochondrial RNA homeostasis.FASTKD1 and FASTKD4 have opposite effects on expression of specific mitochondrial RNAs, depending upon their endonuclease-like RAP domain.LRPPRC and SLIRP interact in a ribonucleoprotein complex that regulates posttranscriptional gene expression in mitochondria.Power Grid Protection of the Muscle Mitochondrial Reticulum.A compendium of human mitochondrial gene expression machinery with links to disease.Leucine-rich pentatricopeptide-repeat containing protein regulates mitochondrial transcription.Genome-wide association analysis identifies a mutation in the thiamine transporter 2 (SLC19A3) gene associated with Alaskan Husky encephalopathyDrosophila melanogaster LRPPRC2 is involved in coordination of mitochondrial translationThe N-terminal domain of the yeast mitochondrial RNA polymerase regulates multiple steps of transcription.A genome wide study in fission yeast reveals nine PPR proteins that regulate mitochondrial gene expression.Long noncoding RNAs are generated from the mitochondrial genome and regulated by nuclear-encoded proteins.Mitochondrial transcript maturation and its disordersGRSF1 regulates RNA processing in mitochondrial RNA granules.The leucine-rich pentatricopeptide repeat-containing protein (LRPPRC) does not activate transcription in mammalian mitochondria.Mitoribosomal regulation of OXPHOS biogenesis in plants.Organization of the human mitochondrial transcription initiation complexModular recognition of nucleic acids by PUF, TALE and PPR proteins.Human pentatricopeptide proteins: only a few and what do they do?Role of FAST Kinase Domains 3 (FASTKD3) in Post-transcriptional Regulation of Mitochondrial Gene Expression.Mouse models for mitochondrial diseases.MRPS27 is a pentatricopeptide repeat domain protein required for the translation of mitochondrially encoded proteins.Adult-onset obesity is triggered by impaired mitochondrial gene expression.Drosophila protease ClpXP specifically degrades DmLRPPRC1 controlling mitochondrial mRNA and translation.LRPPRC-mediated folding of the mitochondrial transcriptome.The mitochondrial transcriptome
P2860
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P248
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P2860
Disruption of a mitochondrial RNA-binding protein gene results in decreased cytochrome b expression and a marked reduction in ubiquinol-cytochrome c reductase activity in mouse heart mitochondria
description
2008 nî lūn-bûn
@nan
2008 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
name
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@ast
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@en
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@en-gb
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@nl
type
label
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@ast
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@en
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@en-gb
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@nl
prefLabel
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@ast
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@en
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@en-gb
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@nl
P2093
P921
P356
P1433
P1476
Disruption of a mitochondrial ...... ty in mouse heart mitochondria
@en
P2093
Brian H Robinson
Cameron Ackerley
Fenghao Xu
Jane B L Addis
Jessie M Cameron
Nevena Mackay
Valeriy Levandovskiy
P356
10.1042/BJ20080847
P407
P50
P577
2008-11-01T00:00:00Z