Taz1, an outer mitochondrial membrane protein, affects stability and assembly of inner membrane protein complexes: implications for Barth Syndrome
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Mitochondrial targeting of electron scavenging antioxidants: regulation of selective oxidation vs random chain reactionsComparison of lymphoblast mitochondria from normal subjects and patients with Barth syndrome using electron microscopic tomographyThe cardiolipin transacylase, tafazzin, associates with two distinct respiratory components providing insight into Barth syndromeCardiolipin membrane domains in prokaryotes and eukaryotesBarth Syndrome: From Mitochondrial Dysfunctions Associated with Aberrant Production of Reactive Oxygen Species to Pluripotent Stem Cell StudiesSuccessful management of Barth syndrome: a systematic review highlighting the importance of a flexible and multidisciplinary approachMetabolism and regulation of glycerolipids in the yeast Saccharomyces cerevisiaeThe translocator maintenance protein Tam41 is required for mitochondrial cardiolipin biosynthesis.Mitochondrial mislocalization and altered assembly of a cluster of Barth syndrome mutant tafazzinsDeacylation on the matrix side of the mitochondrial inner membrane regulates cardiolipin remodeling.Shy1 couples Cox1 translational regulation to cytochrome c oxidase assembly.High confidence proteomic analysis of yeast LDs identifies additional droplet proteins and reveals connections to dolichol synthesis and sterol acetylation.Aim24 and MICOS modulate respiratory function, tafazzin-related cardiolipin modification and mitochondrial architectureThe enzymatic function of tafazzinCardiolipin remodeling by TAZ/tafazzin is selectively required for the initiation of mitophagyMitochondria in heart failureGenome-Wide Screens in Saccharomyces cerevisiae Highlight a Role for Cardiolipin in Biogenesis of Mitochondrial Outer Membrane Multispan ProteinsLipids in the assembly of membrane proteins and organization of protein supercomplexes: implications for lipid-linked disordersDefining functional classes of Barth syndrome mutation in humansDisorders of phospholipid metabolism: an emerging class of mitochondrial disease due to defects in nuclear genesBiosynthesis, remodeling and turnover of mitochondrial cardiolipinThe complexity of cardiolipin in health and diseaseThe topology and regulation of cardiolipin biosynthesis and remodeling in yeastBiogenesis of mitochondrial outer membrane proteins, problems and diseases.Supramolecular organization of the respiratory chain in Neurospora crassa mitochondriaDistinct effects of tafazzin deletion in differentiated and undifferentiated mitochondria.Substrate specificity of the TIM22 mitochondrial import pathway revealed with small molecule inhibitor of protein translocationCoenzyme q and the respiratory chain: coenzyme q pool and mitochondrial supercomplexesAlteration of fatty-acid-metabolizing enzymes affects mitochondrial form and function in hereditary spastic paraplegia.Cardiolipin-based respiratory complex activation in bacteria.Barth syndrome mutations that cause tafazzin complex lability.Mitochondrial cardiolipin involved in outer-membrane protein biogenesis: implications for Barth syndrome.Yeast as a system for modeling mitochondrial disease mechanisms and discovering therapies.Arrangement of the respiratory chain complexes in Saccharomyces cerevisiae supercomplex III2IV2 revealed by single particle cryo-electron microscopy.A novel TAZ gene mutation and mosaicism in a Polish family with Barth syndrome.Tafazzins from Drosophila and mammalian cells assemble in large protein complexes with a short half-life.Cardiac-specific succinate dehydrogenase deficiency in Barth syndromeLoss of cardiolipin leads to perturbation of mitochondrial and cellular iron homeostasisRole of cardiolipin alterations in mitochondrial dysfunction and disease.Barth syndrome, a human disorder of cardiolipin metabolism.
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P2860
Taz1, an outer mitochondrial membrane protein, affects stability and assembly of inner membrane protein complexes: implications for Barth Syndrome
description
2005 nî lūn-bûn
@nan
2005 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2005 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2005年の論文
@ja
2005年論文
@yue
2005年論文
@zh-hant
2005年論文
@zh-hk
2005年論文
@zh-mo
2005年論文
@zh-tw
2005年论文
@wuu
name
Taz1, an outer mitochondrial m ...... mplications for Barth Syndrome
@ast
Taz1, an outer mitochondrial m ...... mplications for Barth Syndrome
@en
Taz1, an outer mitochondrial m ...... plications for Barth Syndrome.
@nl
type
label
Taz1, an outer mitochondrial m ...... mplications for Barth Syndrome
@ast
Taz1, an outer mitochondrial m ...... mplications for Barth Syndrome
@en
Taz1, an outer mitochondrial m ...... plications for Barth Syndrome.
@nl
prefLabel
Taz1, an outer mitochondrial m ...... mplications for Barth Syndrome
@ast
Taz1, an outer mitochondrial m ...... mplications for Barth Syndrome
@en
Taz1, an outer mitochondrial m ...... plications for Barth Syndrome.
@nl
P2093
P2860
P50
P3181
P356
P1476
Taz1, an outer mitochondrial m ...... mplications for Barth Syndrome
@en
P2093
Ann E Frazier
Katrin Brandner
Rebecca D Taylor
P2860
P304
P3181
P356
10.1091/MBC.E05-03-0256
P407
P577
2005-11-01T00:00:00Z