CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
about
Ceramide synthases at the centre of sphingolipid metabolism and biologyEmerging novel concept of chaperone therapies for protein misfolding diseasesLarge-scale phenotyping of an accurate genetic mouse model of JNCL identifies novel early pathology outside the central nervous systemCeramide glycosylation catalyzed by glucosylceramide synthase and cancer drug resistance.A novel interaction of CLN3 with nonmuscle myosin-IIB and defects in cell motility of Cln3(-/-) cellsAssociation between CLN3 (Neuronal Ceroid Lipofuscinosis, CLN3 Type) Gene Expression and Clinical Characteristics of Breast Cancer PatientsAntigen presenting cell abnormalities in the Cln3(-/-) mouse model of juvenile neuronal ceroid lipofuscinosisOsmoregulation of ceroid neuronal lipofuscinosis type 3 in the renal medullaCLN3 loss disturbs membrane microdomain properties and protein transport in brain endothelial cells.Altered dynamics of a lipid raft associated protein in a kidney model of Fabry diseaseLysosomal storage diseases--the horizon expands.Screening for calcium channel modulators in CLN3 siRNA knock down SH-SY5Y neuroblastoma cells reveals a significant decrease of intracellular calcium levels by selected L-type calcium channel blockers.Lipid Involvement in Neurodegenerative Diseases of the Motor System: Insights from Lysosomal Storage Diseases.Pharmacological Effects on Ceroid Lipofuscin and Neuronal Structure in Cln3 ∆ex7/8 Mouse Brain Cultures.Role of the Lysosomal Membrane Protein, CLN3, in the Regulation of Cathepsin D Activity.Altered Expression of Ganglioside Metabolizing Enzymes Results in GM3 Ganglioside Accumulation in Cerebellar Cells of a Mouse Model of Juvenile Neuronal Ceroid Lipofuscinosis.Galactolipid deficiency in the early pathogenesis of neuronal ceroid lipofuscinosis model Cln8mnd : implications to delayed myelination and oligodendrocyte maturation.
P2860
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P2860
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
description
2008 nî lūn-bûn
@nan
2008 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի հունիսին հրատարակված գիտական հոդված
@hy
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
name
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@ast
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@en
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@nl
type
label
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@ast
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@en
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@nl
prefLabel
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@ast
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@en
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@nl
P2093
P2860
P921
P1433
P1476
CLN3p impacts galactosylceramide transport, raft morphology, and lipid content
@en
P2093
Dixie-Ann Persaud-Sawin
Elena Rusyn
Rose-Mary N Boustany
Sara Miller
Talal Mousallem
P2860
P2888
P304
P356
10.1203/PDR.0B013E31816FDC17
P407
P577
2008-06-01T00:00:00Z
P5875
P6179
1041947546