Non-human primate model of amyotrophic lateral sclerosis with cytoplasmic mislocalization of TDP-43
about
Pathological mechanisms underlying TDP-43 driven neurodegeneration in FTLD-ALS spectrum disordersSelective forelimb impairment in rats expressing a pathological TDP-43 25 kDa C-terminal fragment to mimic amyotrophic lateral sclerosis.Protein kinase CK-1 inhibitors as new potential drugs for amyotrophic lateral sclerosis.Expression of ALS-linked TDP-43 mutant in astrocytes causes non-cell-autonomous motor neuron death in ratsMechanisms, models and biomarkers in amyotrophic lateral sclerosisAn effort to use human-based exome capture methods to analyze chimpanzee and macaque exomes.Selection of appropriate reference genes for RT-qPCR analysis in a streptozotocin-induced Alzheimer's disease model of cynomolgus monkeys (Macaca fascicularis).Reversible behavioral phenotypes in a conditional mouse model of TDP-43 proteinopathiesLessons from the analysis of nonhuman primates for understanding human aging and neurodegenerative diseasesInitial gene vector dosing for studying symptomatology of amyotrophic lateral sclerosis in non-human primates.Model systems of motor neuron diseases as a platform for studying pathogenic mechanisms and searching for therapeutic agents.Cytoplasmic mislocalization of RNA splicing factors and aberrant neuronal gene splicing in TDP-43 transgenic pig brain.Entorhinal cortical neurons are the primary targets of FUS mislocalization and ubiquitin aggregation in FUS transgenic rats.XBP1 depletion precedes ubiquitin aggregation and Golgi fragmentation in TDP-43 transgenic rats.Selection of new appropriate reference genes for RT-qPCR analysis via transcriptome sequencing of cynomolgus monkeys (Macaca fascicularis)Disease animal models of TDP-43 proteinopathy and their pre-clinical applications.The advent of AAV9 expands applications for brain and spinal cord gene delivery.Can regional spreading of amyotrophic lateral sclerosis motor symptoms be explained by prion-like propagation?TARDBP and FUS mutations associated with amyotrophic lateral sclerosis: summary and update.Amyotrophic lateral sclerosis: an update on recent genetic insights.Oral biomarkers in exercise-induced neuroplasticity in Parkinson's disease.Rapamycin alleviates pathogenesis of a new Drosophila model of ALS-TDP.Targeted gene transfer into ependymal cells through intraventricular injection of AAV1 vector and long-term enzyme replacement via the CSF.Adenoviral expression of TDP-43 and FUS genes and shRNAs for protein degradation pathways in rodent motoneurons in vitro and in vivo.ALS--dying forward, backward or outward?Platelet phosphorylated TDP-43: an exploratory study for a peripheral surrogate biomarker development for Alzheimer's disease.Activation of the NLRP3 Inflammasome Is Associated with Valosin-Containing Protein Myopathy.Comprehensive Analysis of Circulating microRNA Specific to the Liver, Heart, and Skeletal Muscle of Cynomolgus Monkeys.TDP43 and RNA instability in amyotrophic lateral sclerosis.TDP43 nuclear export and neurodegeneration in models of amyotrophic lateral sclerosis and frontotemporal dementia.
P2860
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P2860
Non-human primate model of amyotrophic lateral sclerosis with cytoplasmic mislocalization of TDP-43
description
2012 nî lūn-bûn
@nan
2012 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
Non-human primate model of amy ...... smic mislocalization of TDP-43
@ast
Non-human primate model of amy ...... smic mislocalization of TDP-43
@en
type
label
Non-human primate model of amy ...... smic mislocalization of TDP-43
@ast
Non-human primate model of amy ...... smic mislocalization of TDP-43
@en
prefLabel
Non-human primate model of amy ...... smic mislocalization of TDP-43
@ast
Non-human primate model of amy ...... smic mislocalization of TDP-43
@en
P2093
P2860
P50
P356
P1433
P1476
Non-human primate model of amy ...... smic mislocalization of TDP-43
@en
P2093
Azusa Uchida
Fumika Sakaue
Fumiko Ono
Hidehiro Mizusawa
Hideki Mochizuki
Hiroki Sasaguri
Jiro Kumagai
Kazuaki Kanai
Kazumoto Shibuya
Kyohei Sakaki
P2860
P304
P356
10.1093/BRAIN/AWR348
P407
P577
2012-01-17T00:00:00Z