Confocal microscopy analysis of native, full length and B-domain deleted coagulation factor VIII trafficking in mammalian cells.
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Gene therapy for hemophiliaChemical chaperones improve protein secretion and rescue mutant factor VIII in mice with hemophilia AThe F309S mutation increases factor VIII secretion in human cell lineEndothelial cell processing and alternatively spliced transcripts of factor VIII: potential implications for coagulation cascades and pulmonary hypertension.Advancements in gene transfer-based therapy for hemophilia A.Quantitative correlation between transcriptional levels of ER chaperone, peroximal protein and FVIII productivity in human Hek-293 cell lineFactor VIII A3 domain substitution N1922S results in hemophilia A due to domain-specific misfolding and hyposecretion of functional proteinComparison of human coagulation factor VIII expression directed by cytomegalovirus and mammary gland-specific promoters in HC11 cells and transgenic miceProduction of recombinant coagulation factors: Are humans the best host cells?
P2860
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P2860
Confocal microscopy analysis of native, full length and B-domain deleted coagulation factor VIII trafficking in mammalian cells.
description
2004 nî lūn-bûn
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2004 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2004 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
2004年の論文
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2004年論文
@yue
2004年論文
@zh-hant
2004年論文
@zh-hk
2004年論文
@zh-mo
2004年論文
@zh-tw
2004年论文
@wuu
name
Confocal microscopy analysis o ...... rafficking in mammalian cells.
@ast
Confocal microscopy analysis o ...... rafficking in mammalian cells.
@en
type
label
Confocal microscopy analysis o ...... rafficking in mammalian cells.
@ast
Confocal microscopy analysis o ...... rafficking in mammalian cells.
@en
prefLabel
Confocal microscopy analysis o ...... rafficking in mammalian cells.
@ast
Confocal microscopy analysis o ...... rafficking in mammalian cells.
@en
P2093
P356
P1476
Confocal microscopy analysis o ...... rafficking in mammalian cells.
@en
P2093
Christian Herder
Erhard Seifried
Jeremy C Simpson
Manuel Grez
Stefan Heinz
Sven Becker
Torsten Tonn
P356
10.1267/THRO04070023
P577
2004-07-01T00:00:00Z