Biochemistry of glycosphingolipid storage disorders: implications for therapeutic intervention
about
Eliglustat tartrate for the treatment of adults with type 1 Gaucher diseaseReducing GBA2 Activity Ameliorates Neuropathology in Niemann-Pick Type C MicePharmacological inhibition of glucosylceramide synthase enhances insulin sensitivitySubstrate reduction therapy: clinical evaluation in type 1 Gaucher disease.Gaucher disease and the clinical experience with substrate reduction therapy.Gaucher disease and its treatment options.Characterization of human phagocyte-derived chitotriosidase, a component of innate immunity.Gaucher disease: pathological mechanisms and modern management.Biomarkers in the diagnosis of lysosomal storage disorders: proteins, lipids, and inhibodies.Future perspectives for glycolipid research in medicine.A historical perspective of the glycosphingolipids and sphingolipidoses.Synthesis and Evaluation of Hybrid Structures Composed of Two Glucosylceramide Synthase Inhibitors.Ganglioside GM1 Contributes to the State of Insulin Resistance in Senescent Human Arterial Endothelial Cells.Successful screening for Gaucher disease in a high-prevalence population in tabuleiro do Norte (northeastern Brazil): a cross-sectional studyPharmacological small molecules for the treatment of lysosomal storage disorders.Ganglioside GM3 as a gatekeeper of obesity-associated insulin resistance: Evidence and mechanisms.The role of ORMDL proteins, guardians of cellular sphingolipids, in asthma.Membrane anchors effectively traffic recombinant human glucocerebrosidase to the protein storage vacuole of Arabidopsis seeds but do not adequately control N-glycan maturation.Novel activity-based probes for broad-spectrum profiling of retaining β-exoglucosidases in situ and in vivo.Ganglioside GM1 contributes to extracellular/intracellular regulation of insulin resistance, impairment of insulin signaling and down-stream eNOS activation, in human aortic endothelial cells after short- or long-term exposure to TNFα.HEPES activates a MiT/TFE-dependent lysosomal-autophagic gene network in cultured cells: A call for caution.
P2860
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P2860
Biochemistry of glycosphingolipid storage disorders: implications for therapeutic intervention
description
2003 nî lūn-bûn
@nan
2003 թուականի Մայիսին հրատարակուած գիտական յօդուած
@hyw
2003 թվականի մայիսին հրատարակված գիտական հոդված
@hy
2003年の論文
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2003年論文
@yue
2003年論文
@zh-hant
2003年論文
@zh-hk
2003年論文
@zh-mo
2003年論文
@zh-tw
2003年论文
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name
Biochemistry of glycosphingoli ...... s for therapeutic intervention
@ast
Biochemistry of glycosphingoli ...... s for therapeutic intervention
@en
type
label
Biochemistry of glycosphingoli ...... s for therapeutic intervention
@ast
Biochemistry of glycosphingoli ...... s for therapeutic intervention
@en
prefLabel
Biochemistry of glycosphingoli ...... s for therapeutic intervention
@ast
Biochemistry of glycosphingoli ...... s for therapeutic intervention
@en
P2860
P356
P1476
Biochemistry of glycosphingoli ...... s for therapeutic intervention
@en
P2093
Ans Groener
Carla Hollak
P2860
P304
P356
10.1098/RSTB.2003.1273
P407
P577
2003-05-01T00:00:00Z