Pulmonary vascular manifestations of hereditary hemorrhagic telangiectasia (rendu-osler disease).
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Hereditary hemorrhagic telangiectasia: an overview of diagnosis, management, and pathogenesisBone morphogenetic protein 2 induces pulmonary angiogenesis via Wnt-beta-catenin and Wnt-RhoA-Rac1 pathways.Constitutively active endothelial Notch4 causes lung arteriovenous shunts in mice.Stroke in hereditary hemorrhagic telangiectasia patients. New evidence for repeated screening and early treatment of pulmonary vascular malformations: two case reportsGenetic predisposition to respiratory diseases: infiltrative lung diseases.Complications and mortality in hereditary hemorrhagic telangiectasia: A population-based study.The intersection of genes and environment: development of pulmonary arterial hypertension in a patient with hereditary hemorrhagic telangiectasia and stimulant exposure.Mouse and human strategies identify PTPN14 as a modifier of angiogenesis and hereditary haemorrhagic telangiectasia.Endoglin: a critical mediator of cardiovascular healthPulmonary arteriovenous malformations and migraine: a new vision.A mutation in TTF1/NKX2.1 is associated with familial neuroendocrine cell hyperplasia of infancy.The pathogenesis of aortopathy in Marfan syndrome and related diseases.Management of a solitary pulmonary arteriovenous malformation by video-assisted thoracoscopic surgery and anatomic lingula resection: video and review.The rendu-osler-weber disease revealed by a refractory hypoxemia and severe cerebral fat embolism.Case Report: Brown Fat Accumulation of Tc-99m Macroaggregated Albumin in a Lung Perfusion Study in a Patient With Multiple Lung Arteriovenous Malformations and Right-to-Left Shunting.Pulmonary hypertension in a patient with hereditary haemorrhagic telangiectasiaBirt-Hogg-Dube syndrome accompanied by pulmonary arteriovenous malformationPulmonary hypertension subtypes associated with hereditary haemorrhagic telangiectasia: Haemodynamic profiles and survival probabilityAn interesting case of cerebral abscess.Editorial Commentary: Understanding Marfan syndrome, or "how not to invent the light bulb".Expression of angiogenic and vasculogenic proteins in the lung in alveolar capillary dysplasia/misalignment of pulmonary veins: an immunohistochemical study.Age-dependent endothelial nitric oxide synthase uncoupling in pulmonary arteries of endoglin heterozygous mice.Hereditary haemorrhagic telangiectasia, an Australian cohort: clinical and investigative features.Non-invasive CT screening for pulmonary arteriovenous malformations in children with confirmed hereditary hemorrhagic telangiectasia: Results from two pediatric centers.First use of Micro Vascular Plugs in Australia: Endovascular treatment of pulmonary arteriovenous malformation.Characterization of pulmonary arteriovenous malformations in ACVRL1 versus ENG mutation carriers in hereditary hemorrhagic telangiectasia.The Lung in Hereditary Hemorrhagic Telangiectasia.A case of intrapulmonary transmission of air while transitioning a patient from a sitting to a supine position after venous air embolism during a craniotomy.Heart failure and pulmonary arteriovenous malformations in a patient with hereditary hemorrhagic telangiectasia type 2.Hereditary hemorrhagic telangiectasia with multiple hepatic and pulmonary nodular lesions.Cerebrovascular complications in a patient with hereditary hemorrhagic telangiectasia (HHT, Rendu-Osler disease).A pulmonary arteriovenous malformation growing for 35 years comes to an end.Different features of pulmonary hypertension in Rendu-Osler Syndrome.A case report of hepatopulmonary syndrome in hereditary hemorrhagic telangiectasia (HHT): Not all right-to-left shunting in HHT is due to pulmonary arteriovenous malformationsClinical features and treatment of hereditary hemorrhagic telangiectasia
P2860
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P2860
Pulmonary vascular manifestations of hereditary hemorrhagic telangiectasia (rendu-osler disease).
description
2007 nî lūn-bûn
@nan
2007年の論文
@ja
2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
2007年论文
@zh
2007年论文
@zh-cn
name
Pulmonary vascular manifestati ...... ectasia (rendu-osler disease).
@en
type
label
Pulmonary vascular manifestati ...... ectasia (rendu-osler disease).
@en
prefLabel
Pulmonary vascular manifestati ...... ectasia (rendu-osler disease).
@en
P2093
P2860
P356
P1433
P1476
Pulmonary vascular manifestati ...... ectasia (rendu-osler disease).
@en
P2093
Gaetan Lesca
Jean-François Cordier
Sophie Dupuis-Girod
Vincent Cottin
P2860
P304
P356
10.1159/000103205
P577
2007-01-01T00:00:00Z