Characterization of New Transgenic Mouse Models for Two Charcot-Marie-Tooth-Causing HspB1 Mutations using the Rosa26 Locus.
about
HSPB1 mutations causing hereditary neuropathy in humans disrupt non-cell autonomous protection of motor neurons.A knock-in/knock-out mouse model of HSPB8-associated distal hereditary motor neuropathy and myopathy reveals toxic gain-of-function of mutant Hspb8.Mitochondrial deficits and abnormal mitochondrial retrograde axonal transport play a role in the pathogenesis of mutant Hsp27-induced Charcot Marie Tooth Disease.
P2860
Characterization of New Transgenic Mouse Models for Two Charcot-Marie-Tooth-Causing HspB1 Mutations using the Rosa26 Locus.
description
2016 nî lūn-bûn
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2016年の論文
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2016年学术文章
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2016年学术文章
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2016年学术文章
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2016年学术文章
@zh-hans
2016年学术文章
@zh-my
2016年学术文章
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2016年學術文章
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2016年學術文章
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name
Characterization of New Transg ...... ations using the Rosa26 Locus.
@en
Characterization of New Transg ...... ations using the Rosa26 Locus.
@nl
type
label
Characterization of New Transg ...... ations using the Rosa26 Locus.
@en
Characterization of New Transg ...... ations using the Rosa26 Locus.
@nl
prefLabel
Characterization of New Transg ...... ations using the Rosa26 Locus.
@en
Characterization of New Transg ...... ations using the Rosa26 Locus.
@nl
P2093
P2860
P50
P356
P1476
Characterization of New Transg ...... tations using the Rosa26 Locus
@en
P2093
Delphine Bouhy
Joachim Weis
Jody J Haigh
Sophie Janssens
Tino Hochepied
Vicky De Winter
Vincent Timmerman
P2860
P304
P356
10.3233/JND-150144
P577
2016-05-01T00:00:00Z