Triplet repeat-derived siRNAs enhance RNA-mediated toxicity in a Drosophila model for myotonic dystrophy
about
Myotonic dystrophy: is a narrow focus obscuring the rest of the field?Structural studies of CNG repeatsMechanisms of RNA-induced toxicity in CAG repeat disordersRNA-mediated pathogenic mechanisms in polyglutamine diseases and amyotrophic lateral sclerosisMyotonic Dystrophies: State of the Art of New Therapeutic Developments for the CNS.A pathogenic mechanism in Huntington's disease involves small CAG-repeated RNAs with neurotoxic activity.C9orf72 amyotrophic lateral sclerosis and frontotemporal dementia: gain or loss of function?Ubiquitous expression of CUG or CAG trinucleotide repeat RNA causes common morphological defects in a Drosophila model of RNA-mediated pathologyHigh-content screening identifies small molecules that remove nuclear foci, affect MBNL distribution and CELF1 protein levels via a PKC-independent pathway in myotonic dystrophy cell lines.Characterisation of the small RNAs in the biomedically important green-bottle blowfly Lucilia sericata.Triplet repeat RNA structure and its role as pathogenic agent and therapeutic targetNeurodegeneration the RNA wayEpigenetics in Friedreich's Ataxia: Challenges and Opportunities for Therapy.RNA toxicity in polyglutamine disorders: concepts, models, and progress of researchThe Enemy within: Innate Surveillance-Mediated Cell Death, the Common Mechanism of Neurodegenerative Disease.Distinct roles for Toll and autophagy pathways in double-stranded RNA toxicity in a Drosophila model of expanded repeat neurodegenerative diseases.Bidirectional transcription of trinucleotide repeats: roles for excision repair.RNA pathogenesis via Toll-like receptor-activated inflammation in expanded repeat neurodegenerative diseases.RNA-mediated toxicity in neurodegenerative diseaseDrosophila melanogaster As a Model Organism to Study RNA Toxicity of Repeat Expansion-Associated Neurodegenerative and Neuromuscular DiseasesRole of noncoding RNAs in trinucleotide repeat neurodegenerative disorders.Small non-coding RNAs add complexity to the RNA pathogenic mechanisms in trinucleotide repeat expansion diseases.Mechanisms of transcriptional dysregulation in repeat expansion disorders.Structure and Dynamics of RNA Repeat Expansions That Cause Huntington's Disease and Myotonic Dystrophy Type 1.RNA toxicity induced by expanded CAG repeats in Huntington's disease.The role of RNA metabolism in neurological diseases.Antisense transcription of the myotonic dystrophy locus yields low-abundant RNAs with and without (CAG)n repeat.Small interfering RNAs based on huntingtin trinucleotide repeats are highly toxic to cancer cells.Small molecule alteration of RNA sequence in cells and animals.A fly model for the CCUG-repeat expansion of myotonic dystrophy type 2 reveals a novel interaction with MBNL1.Bruno-3 regulates sarcomere component expression and contributes to muscle phenotypes of myotonic dystrophy type 1.
P2860
Q26830455-AFAB06EB-D5BB-4F45-AE92-AE24699F857AQ26851232-B03A9083-DE73-4E08-A376-F3A172AA44A0Q26860030-6C50FB3A-6195-46E6-89EF-AD388E20729DQ28082520-1923FE0B-0988-49E5-A1A8-722AF1A7484AQ33580885-AF7A4624-D245-4BD5-A4D5-B0BD9FDD4A9BQ34181368-BE21ABA9-8CAB-44FF-84A3-982865A797E5Q34194063-03E0F9FC-25BB-4B6D-B82C-E7AB78D88C38Q34310291-EAB83DA4-5C4A-44F1-A400-F92DBB4939F1Q35030106-878328F4-278A-4A82-8085-87B09D09DD1BQ35214285-DCF65E68-E7A2-49F9-A2FF-5641682405CFQ35633648-891F6106-FCD1-44BD-84DA-EA7E566B60FEQ36638284-8EC0B6C5-9FEE-43AA-87AB-4B13EB50FDBEQ36663928-E7FCEF49-4D31-445B-A500-6273D9CAA93FQ36859984-12A4253F-8E64-4C95-8F10-85FC6AC7C18FQ36887309-81A05F45-CA2D-4B14-B605-EAF69C428A21Q36950670-30447DB9-F8DC-4972-80FD-DC5818803176Q37038917-1627974F-E86F-4B70-90DC-1BC54FAEB8C5Q37148589-C12A0A21-11EE-4A21-AF66-D00BE5CC7268Q37216891-2D642A2B-63E9-4D83-A19C-0C316043559BQ37713198-AEDD28EE-1A48-4258-B0D5-0ECD9C5E231AQ37981785-65F6DE3F-277D-4147-8A92-99D2EFDF0626Q38172118-26BF2CF8-F787-488F-BEE5-10C953D61DFEQ38238667-3BCDB419-B11C-4D70-8219-BDE4E801B37BQ38430517-E07103D1-EF81-4F8B-BFA8-4CD801520009Q38928719-8344939F-D232-4ED1-8C2F-4440DCA52F0BQ38992087-9C7BF775-C91C-4D6D-900D-851D32038483Q39012706-54C4ACAA-5B78-4700-9BCD-F7C59CCD7B7CQ50027519-4897D8BE-017F-41BA-A38B-DFBE4EE39DE8Q50100221-A059DD91-105E-4F73-B642-53D2EB27F823Q52780616-EC8C7DA9-9DB4-43D4-93CE-EE4CA83B713FQ55322911-6CB5FF1A-0FC3-4D64-BE84-65A9F91EC137
P2860
Triplet repeat-derived siRNAs enhance RNA-mediated toxicity in a Drosophila model for myotonic dystrophy
description
2011 nî lūn-bûn
@nan
2011 թուականի Մարտին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի մարտին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@ast
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@en
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@nl
type
label
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@ast
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@en
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@nl
altLabel
Triplet Repeat–Derived siRNAs ...... a Model for Myotonic Dystrophy
@en
prefLabel
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@ast
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@en
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@nl
P2860
P3181
P1433
P1476
Triplet repeat-derived siRNAs ...... a model for myotonic dystrophy
@en
P2093
Xiuyin Teng
Zhenming Yu
P2860
P304
P3181
P356
10.1371/JOURNAL.PGEN.1001340
P407
P577
2011-03-17T00:00:00Z