AAV-mediated overexpression of human α7 integrin leads to histological and functional improvement in dystrophic mice
about
Current and emerging treatment strategies for Duchenne muscular dystrophyAnimal models of Duchenne muscular dystrophy: from basic mechanisms to gene therapyNew insights into the mechanisms of gene electrotransfer--experimental and theoretical analysisSarcospan integration into laminin-binding adhesion complexes that ameliorate muscular dystrophy requires utrophin and α7 integrin.Progress and prospects of gene therapy clinical trials for the muscular dystrophies.AAV.Dysferlin Overlap Vectors Restore Function in Dysferlinopathy Animal ModelsIn vivo assessment of contractile strength distinguishes differential gene function in skeletal muscle of zebrafish larvae.Absence of Dystrophin Disrupts Skeletal Muscle Signaling: Roles of Ca2+, Reactive Oxygen Species, and Nitric Oxide in the Development of Muscular Dystrophy.Prospect of gene therapy for cardiomyopathy in hereditary muscular dystrophy.Alpha 7 integrin preserves the function of the extensor digitorum longus muscle in dystrophin-null mice.Micro-dystrophin and follistatin co-delivery restores muscle function in aged DMD model.Current Translational Research and Murine Models For Duchenne Muscular Dystrophy.Pathoproteomic profiling of the skeletal muscle matrisome in dystrophinopathy associated myofibrosis.Systemic Delivery of Dysferlin Overlap Vectors Provides Long-Term Gene Expression and Functional Improvement for Dysferlinopathy.Nanotherapy for Duchenne muscular dystrophy.Deletion of integrin α7 subunit does not aggravate the phenotype of laminin α2 chain-deficient mice.Human α7 Integrin Gene (ITGA7) Delivered by Adeno-Associated Virus Extends Survival of Severely Affected Dystrophin/Utrophin-Deficient MiceDisease-modifying effects of orally bioavailable NF-κB inhibitors in dystrophin-deficient muscle
P2860
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P2860
AAV-mediated overexpression of human α7 integrin leads to histological and functional improvement in dystrophic mice
description
2013 nî lūn-bûn
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2013 թուականի Մարտին հրատարակուած գիտական յօդուած
@hyw
2013 թվականի մարտին հրատարակված գիտական հոդված
@hy
2013年の論文
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2013年論文
@yue
2013年論文
@zh-hant
2013年論文
@zh-hk
2013年論文
@zh-mo
2013年論文
@zh-tw
2013年论文
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name
AAV-mediated overexpression of ...... improvement in dystrophic mice
@ast
AAV-mediated overexpression of ...... improvement in dystrophic mice
@en
AAV-mediated overexpression of ...... improvement in dystrophic mice
@nl
type
label
AAV-mediated overexpression of ...... improvement in dystrophic mice
@ast
AAV-mediated overexpression of ...... improvement in dystrophic mice
@en
AAV-mediated overexpression of ...... improvement in dystrophic mice
@nl
prefLabel
AAV-mediated overexpression of ...... improvement in dystrophic mice
@ast
AAV-mediated overexpression of ...... improvement in dystrophic mice
@en
AAV-mediated overexpression of ...... improvement in dystrophic mice
@nl
P2093
P2860
P3181
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P1476
AAV-mediated overexpression of ...... improvement in dystrophic mice
@en
P2093
Chrystal L Montgomery
Jerry R Mendell
K Reed Clark
Kristin N Heller
Louise R Rodino-Klapac
P2860
P304
P3181
P356
10.1038/MT.2012.281
P407
P577
2013-01-15T00:00:00Z