Phospholipid synthesis is decreased in neuronal tissue in a mouse model of Sandhoff disease
about
Genetic diseases of sphingolipid metabolism: pathological mechanisms and therapeutic options.Protease-resistant modified human β-hexosaminidase B ameliorates symptoms in GM2 gangliosidosis modelSphingosine kinase 1/S1P receptor signaling axis controls glial proliferation in mice with Sandhoff disease.Lipid content of brain, brain membrane lipid domains, and neurons from acid sphingomyelinase deficient mice.Reversibility of neuropathology in Tay-Sachs-related diseases.Metabolic Dysfunction of Astrocyte: An Initiating Factor in Beta-amyloid Pathology?Lysosomal storage disease: revealing lysosomal function and physiology.Role of phosphatidylcholine during neuronal differentiation.Metabolic correction in microglia derived from Sandhoff disease model mice.Defective calcium homeostasis in the cerebellum in a mouse model of Niemann-Pick A disease.Neuronal pentraxin 1 depletion delays neurodegeneration and extends life in Sandhoff disease mice.
P2860
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P2860
Phospholipid synthesis is decreased in neuronal tissue in a mouse model of Sandhoff disease
description
2004 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2004 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
artículu científicu espublizáu en 2004
@ast
scientific journal article
@en
vedecký článok (publikovaný 2004/07/01)
@sk
vědecký článek publikovaný v roce 2004
@cs
wetenschappelijk artikel (gepubliceerd op 2004/07/01)
@nl
наукова стаття, опублікована в липні 2004
@uk
مقالة علمية (نشرت في يوليو 2004)
@ar
name
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@ast
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@en
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@nl
type
label
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@ast
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@en
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@nl
prefLabel
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@ast
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@en
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@nl
P2093
P1476
Phospholipid synthesis is decr ...... ouse model of Sandhoff disease
@en
P2093
Gerhild Van Echten-Deckert
Jacques Bodennec
Konrad Sandhoff
Rosaria Buccoliero
P2860
P356
10.1111/J.1471-4159.2004.02457.X
P407
P577
2004-07-01T00:00:00Z