about
A mitochondrial protein compendium elucidates complex I disease biologyTruncated product of the bifunctional DLST gene involved in biogenesis of the respiratory chainCardiomyopathy in Friedreich ataxia: clinical findings and researchMitochondrial genome changes and neurodegenerative diseasesPathogenesis of ataxia-telangiectasia: the next generation of ATM functionsModes of metabolic compensation during mitochondrial disease using the Drosophila model of ATP6 dysfunctionThe G336S variant in the human neurofilament-M gene does not affect its assembly or distribution: importance of the functional analysis of neurofilament variantsTransgenic control of mitochondrial fission induces mitochondrial uncoupling and relieves diabetic oxidative stress.A Drosophila model of mitochondrial disease caused by a complex I mutation that uncouples proton pumping from electron transfer.Validation of microarray data in human lymphoblasts shows a role of the ubiquitin-proteasome system and NF-kB in the pathogenesis of Down syndrome.Neuroprotection by a mitochondria-targeted drug in a Parkinson's disease modelSilybum marianum oil attenuates oxidative stress and ameliorates mitochondrial dysfunction in mice treated with D-galactose.Mitochondrial dysfunction in the striatum of aged chronic mouse model of Parkinson's disease.Mitochondrial dysfunction links ceramide activated HRK expression and cell death.The metabolic enhancer piracetam ameliorates the impairment of mitochondrial function and neurite outgrowth induced by beta-amyloid peptideThe neurodegenerative mitochondriopathies.Oxidative stress, mitochondrial damage and neurodegenerative diseasesComplex I deficiency primes Bax-dependent neuronal apoptosis through mitochondrial oxidative damageImpaired mitochondrial respiration and protein nitration in the rat hippocampus after acute inhalation of combustion smoke.Homozygosity mapping of Marinesco-Sjögren syndrome to 5q31.Neuronal inactivation of peroxisome proliferator-activated receptor γ coactivator 1α (PGC-1α) protects mice from diet-induced obesity and leads to degenerative lesionsIn vivo quantification reveals extensive natural variation in mitochondrial form and function in Caenorhabditis briggsae.Modeling mitochondrial function and its role in disease.Disruption of adaptive energy metabolism and elevated ribosomal p-S6K1 levels contribute to INCL pathogenesis: partial rescue by resveratrolAre maternal mitochondria the selfish entities that are masters of the cells of eukaryotic multicellular organisms?Effects of astaxanthin-rich Haematococcus pluvialis extract on cognitive function: a randomised, double-blind, placebo-controlled study.Parkin ubiquitinates Drp1 for proteasome-dependent degradation: implication of dysregulated mitochondrial dynamics in Parkinson diseaseMedication-induced mitochondrial damage and disease.Neurodegeneration: what is it and where are we?Genetic and cellular studies of oxidative stress in methylmalonic aciduria (MMA) cobalamin deficiency type C (cblC) with homocystinuria (MMACHC).Genetics and mitochondrial abnormalities in autism spectrum disorders: a review.The striatum is highly susceptible to mitochondrial oxidative phosphorylation dysfunctionsIRS2 increases mitochondrial dysfunction and oxidative stress in a mouse model of Huntington diseaseRoles of oxidative stress, apoptosis, PGC-1α and mitochondrial biogenesis in cerebral ischemia.Mitochondrial encephalomyopathies: therapeutic approach.Sustained expression of PGC-1α in the rat nigrostriatal system selectively impairs dopaminergic function.Time-Dependent Progression of Demyelination and Axonal Pathology in MP4-Induced Experimental Autoimmune Encephalomyelitis.Proteomic Profiling in the Brain of CLN1 Disease Model Reveals Affected Functional Modules.Assessment and treatment in autism spectrum disorders: a focus on genetics and psychiatryMitochondrial DNA and disease.
P2860
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P2860
description
2003 nî lūn-bûn
@nan
2003 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
2003 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
2003年の論文
@ja
2003年論文
@yue
2003年論文
@zh-hant
2003年論文
@zh-hk
2003年論文
@zh-mo
2003年論文
@zh-tw
2003年论文
@wuu
name
Neuronal degeneration and mitochondrial dysfunction.
@ast
Neuronal degeneration and mitochondrial dysfunction.
@en
type
label
Neuronal degeneration and mitochondrial dysfunction.
@ast
Neuronal degeneration and mitochondrial dysfunction.
@en
prefLabel
Neuronal degeneration and mitochondrial dysfunction.
@ast
Neuronal degeneration and mitochondrial dysfunction.
@en
P2860
P356
P1476
Neuronal degeneration and mitochondrial dysfunction.
@en
P2093
Eric A Schon
Giovanni Manfredi
P2860
P304
P356
10.1172/JCI200317741
P407
P577
2003-02-01T00:00:00Z