Cardiac elav-type RNA-binding protein (ETR-3) binds to RNA CUG repeats expanded in myotonic dystrophy
about
A family of human RNA-binding proteins related to the Drosophila Bruno translational regulatorCharacterisation of human adenylyl cyclase IX reveals inhibition by Ca(2+)/Calcineurin and differential mRNA plyadenylationThe CELF family of RNA binding proteins is implicated in cell-specific and developmentally regulated alternative splicingCUG-BP binds to RNA substrates and recruits PARN deadenylaseMolecular basis for impaired muscle differentiation in myotonic dystrophyETR-3 and CELF4 protein domains required for RNA binding and splicing activity in vivoHuman sat III and Drosophila hsr omega transcripts: a common paradigm for regulation of nuclear RNA processing in stressed cellsHnRNP H inhibits nuclear export of mRNA containing expanded CUG repeats and a distal branch point sequence.The importance of CELF control: molecular and biological roles of the CUG-BP, Elav-like family of RNA-binding proteinsRNA CUG repeats sequester CUGBP1 and alter protein levels and activity of CUGBP1Novel role for RNA-binding protein CUGBP2 in mammalian RNA editing. CUGBP2 modulates C to U editing of apolipoprotein B mRNA by interacting with apobec-1 and ACF, the apobec-1 complementation factorRNA binding protein CUGBP2/CELF2 mediates curcumin-induced mitotic catastrophe of pancreatic cancer cells.Myotonic dystrophy: the role of RNA CUG triplet repeats.RNA structure of trinucleotide repeats associated with human neurological diseases.Molecular characterization of the mouse In(10)17Rk inversion and identification of a novel muscle-specific gene at the proximal breakpoint.Whole genome association study identifies polymorphisms associated with QT prolongation during iloperidone treatment of schizophrenia.Myotonic dystrophy type 2.Structures of trinucleotide repeats in human transcripts and their functional implications.Novel intestinal splice variants of RNA-binding protein CUGBP2: isoform-specific effects on mitotic catastrophe.Myotonic dystrophy: RNA pathogenesis comes into focus.RNA Structures as Mediators of Neurological Diseases and as Drug Targets.Mutant DMPK 3'-UTR transcripts disrupt C2C12 myogenic differentiation by compromising MyoD.Association of CELF2 polymorphism and the prognosis of nasopharyngeal carcinoma in southern Chinese population.Misregulation of alternative splicing causes pathogenesis in myotonic dystrophy.CELF RNA binding proteins promote axon regeneration in C. elegans and mammals through alternative splicing of Syntaxins.Identifying proteins that bind to specific RNAs - focus on simple repeat expansion diseases.Muscular myopathies other than myotonic dystrophy also associated with (CTG)n expansion at the DMPK locus.SRp20 and CUG-BP1 modulate insulin receptor exon 11 alternative splicing.Role of RNA-Binding Proteins in Colorectal Carcinogenesis.The circadian RNA-binding protein CHLAMY 1 represents a novel type heteromer of RNA recognition motif and lysine homology domain-containing subunits.Aromatic side-chain conformational switch on the surface of the RNA Recognition Motif enables RNA discrimination.Region-specific alternative splicing in the nervous system: implications for regulation by the RNA-binding protein NAPOR.Antagonistic regulation of alpha-actinin alternative splicing by CELF proteins and polypyrimidine tract binding protein.Regulation of alternative splicing of alpha-actinin transcript by Bruno-like proteins.Expanded CTG repeats trigger miRNA alterations in Drosophila that are conserved in myotonic dystrophy type 1 patients.
P2860
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P2860
Cardiac elav-type RNA-binding protein (ETR-3) binds to RNA CUG repeats expanded in myotonic dystrophy
description
1999 nî lūn-bûn
@nan
1999 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
1999 թվականի հունվարին հրատարակված գիտական հոդված
@hy
1999年の論文
@ja
1999年学术文章
@wuu
1999年学术文章
@zh-cn
1999年学术文章
@zh-hans
1999年学术文章
@zh-my
1999年学术文章
@zh-sg
1999年學術文章
@yue
name
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@ast
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@en
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@en-gb
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@nl
type
label
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@ast
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@en
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@en-gb
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@nl
prefLabel
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@ast
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@en
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@en-gb
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@nl
P2093
P3181
P356
P1476
Cardiac elav-type RNA-binding ...... expanded in myotonic dystrophy
@en
P2093
L T Timchenko
N A Timchenko
P3181
P356
10.1093/HMG/8.1.53
P407
P577
1999-01-01T00:00:00Z