Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
about
Mpl traffics to the cell surface through conventional and unconventional routesGRASP: A Multitasking TetherDual roles for autophagy: degradation and secretion of Alzheimer's disease Aβ peptideExpanding proteostasis by membrane trafficking networksWhere is it and How Does it Get There - Intracellular Localization and Traffic of P-glycoproteinSecretory autophagyA functional CFTR assay using primary cystic fibrosis intestinal organoidsSphingosine-1-Phosphate Is a Novel Regulator of Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) ActivityAutophagy-based unconventional secretory pathway for extracellular delivery of IL-1βZebrafish Models for the Mechanosensory Hair Cell Dysfunction in Usher Syndrome 3 Reveal That Clarin-1 Is an Essential Hair Bundle Protein.Loss of a Clueless-dGRASP complex results in ER stress and blocks Integrin exit from the perinuclear endoplasmic reticulum in Drosophila larval muscle.A small molecule mitigates hearing loss in a mouse model of Usher syndrome IIIThe ΔF508-CFTR mutation inhibits wild-type CFTR processing and function when co-expressed in human airway epithelia and in mouse nasal mucosa.Genetic, structural, and chemical insights into the dual function of GRASP55 in germ cell Golgi remodeling and JAM-C polarized localization during spermatogenesis.A CULLINary ride across the secretory pathway: more than just secretion.Stabilizing rescued surface-localized δf508 CFTR by potentiation of its interaction with Na(+)/H(+) exchanger regulatory factor 1.Molecular pathogenesis of spondylocheirodysplastic Ehlers-Danlos syndrome caused by mutant ZIP13 proteins.Pharmacological Correctors of Mutant CFTR Mistrafficking.Rescue of murine F508del CFTR activity in native intestine by low temperature and proteasome inhibitorsInsulin-like growth factor 1 (IGF-1) enhances the protein expression of CFTR.Subcellular sorting of the G-protein coupled mouse somatostatin receptor 5 by a network of PDZ-domain containing proteins.Regulation of ABCC6 trafficking and stability by a conserved C-terminal PDZ-like sequenceIntracellular Na+ regulates epithelial Na+ channel maturation.Genetic Inhibition Of The Ubiquitin Ligase Rnf5 Attenuates Phenotypes Associated To F508del Cystic Fibrosis Mutation.Intracellular trafficking of P-glycoprotein.The unfolded protein response regulates an angiogenic response by the kidney epithelium during ischemic stressEndoproteolytic cleavage of TUG protein regulates GLUT4 glucose transporter translocationCapturing the Direct Binding of CFTR Correctors to CFTR by Using Click Chemistry.Modular organization of the mammalian Golgi apparatusSequential phosphorylation of GRASP65 during mitotic Golgi disassembly.Reduced PDZ interactions of rescued ΔF508CFTR increases its cell surface mobility.Dynamic modulation of ANO1/TMEM16A HCO3(-) permeability by Ca2+/calmodulin.Targeting the Intracellular Environment in Cystic Fibrosis: Restoring Autophagy as a Novel Strategy to Circumvent the CFTR Defect.Secreted Acb1 Contributes to the Yeast-to-Hypha Transition in Cryptococcus neoformansRegulation of protein glycosylation and sorting by the Golgi matrix proteins GRASP55/65.PRPH2/RDS and ROM-1: Historical context, current views and future considerations.The HSP70 co-chaperone DNAJC14 targets misfolded pendrin for unconventional protein secretion.ESCRT-III drives the final stages of CUPS maturation for unconventional protein secretion.Functional characterization of ABCB4 mutations found in progressive familial intrahepatic cholestasis type 3Secretory versus degradative autophagy: unconventional secretion of inflammatory mediators
P2860
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P2860
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
description
2011 nî lūn-bûn
@nan
2011 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@ast
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@en
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@en-gb
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@nl
type
label
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@ast
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@en
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@en-gb
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@nl
prefLabel
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@ast
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@en
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@en-gb
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@nl
P2093
P921
P3181
P1433
P1476
Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway
@en
P2093
Bor Luen Tang
Heon Yung Gee
Kyung Hwan Kim
Shin Hye Noh
P304
P3181
P356
10.1016/J.CELL.2011.07.021
P407
P50
P577
2011-09-02T00:00:00Z