An interaction between frataxin and Isu1/Nfs1 that is crucial for Fe/S cluster synthesis on Isu1.
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Dynamics, stability and iron-binding activity of frataxin clinical mutantsFrataxin-mediated iron delivery to ferrochelatase in the final step of heme biosynthesisUnderstanding the genetic and molecular pathogenesis of Friedreich's ataxia through animal and cellular modelsErythropoietin in Friedreich ataxiaThe role of mitochondria in cellular iron-sulfur protein biogenesis: mechanisms, connected processes, and diseasesUnderstanding the binding properties of an unusual metal-binding protein--a study of bacterial frataxinFriedreich’s Ataxia Variants I154F and W155R Diminish Frataxin-Based Activation of the Iron–Sulfur Cluster Assembly ComplexInteraction of J-Protein Co-Chaperone Jac1 with Fe–S Scaffold Isu Is Indispensable In Vivo and Conserved in EvolutionComponents involved in assembly and dislocation of iron-sulfur clusters on the scaffold protein Isu1pA specific role of the yeast mitochondrial carriers MRS3/4p in mitochondrial iron acquisition under iron-limiting conditions.Monomeric yeast frataxin is an iron-binding protein.Essential role of Isd11 in mitochondrial iron-sulfur cluster synthesis on Isu scaffold proteins.Yeast aconitase in two locations and two metabolic pathways: seeing small amounts is believingThe yeast scaffold proteins Isu1p and Isu2p are required inside mitochondria for maturation of cytosolic Fe/S proteinsThe Cfd1-Nbp35 complex acts as a scaffold for iron-sulfur protein assembly in the yeast cytosol.Mitochondrial Iba57p is required for Fe/S cluster formation on aconitase and activation of radical SAM enzymes.The Nfs1 interacting protein Isd11 has an essential role in Fe/S cluster biogenesis in mitochondria.Mitochondrial functional interactions between frataxin and Isu1p, the iron-sulfur cluster scaffold protein, in Saccharomyces cerevisiae.Acidic residues of yeast frataxin have an essential role in Fe-S cluster assembly.Role of Nfu1 and Bol3 in iron-sulfur cluster transfer to mitochondrial clients.The Friedreich's ataxia protein frataxin modulates DNA base excision repair in prokaryotes and mammalsTurning Escherichia coli into a Frataxin-Dependent OrganismFrataxin is essential for extramitochondrial Fe-S cluster proteins in mammalian tissuesStructural, Mechanistic and Coordination Chemistry of Relevance to the Biosynthesis of Iron-Sulfur and Related Iron CofactorsThe role of CyaY in iron sulfur cluster assembly on the E. coli IscU scaffold protein.Autosomal recessive cerebellar ataxias.In silico pathway reconstruction: Iron-sulfur cluster biogenesis in Saccharomyces cerevisiae.Effects of the deletion of the Escherichia coli frataxin homologue CyaY on the respiratory NADH:ubiquinone oxidoreductaseThe in vivo mitochondrial two-step maturation of human frataxin.Limitations in a frataxin knockdown cell model for Friedreich ataxia in a high-throughput drug screenFlavin adenine dinucleotide rescues the phenotype of frataxin deficiency.Mutation in the Fe-S scaffold protein Isu bypasses frataxin deletion.Frataxin-bypassing Isu1: characterization of the bypass activity in cells and mitochondriaFunctions and cellular localization of cysteine desulfurase and selenocysteine lyase in Trypanosoma brucei.Mitochondrial dysfunction induced by frataxin deficiency is associated with cellular senescence and abnormal calcium metabolismGAA repeat expansion mutation mouse models of Friedreich ataxia exhibit oxidative stress leading to progressive neuronal and cardiac pathology.The structure and function of frataxin.Mammalian frataxin: an essential function for cellular viability through an interaction with a preformed ISCU/NFS1/ISD11 iron-sulfur assembly complex.Iron-binding activity of human iron-sulfur cluster assembly protein hIscA1Gene expression profiling in frataxin deficient mice: microarray evidence for significant expression changes without detectable neurodegeneration
P2860
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P2860
An interaction between frataxin and Isu1/Nfs1 that is crucial for Fe/S cluster synthesis on Isu1.
description
2003 nî lūn-bûn
@nan
2003 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
2003 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
2003年の論文
@ja
2003年論文
@yue
2003年論文
@zh-hant
2003年論文
@zh-hk
2003年論文
@zh-mo
2003年論文
@zh-tw
2003年论文
@wuu
name
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@ast
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@en
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@nl
type
label
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@ast
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@en
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@nl
prefLabel
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@ast
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@en
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@nl
P2860
P3181
P1433
P1476
An interaction between frataxi ...... e/S cluster synthesis on Isu1.
@en
P2093
Jana Gerber
Ulrich Mühlenhoff
P2860
P304
P3181
P356
10.1038/SJ.EMBOR.EMBOR918
P407
P577
2003-08-15T00:00:00Z