Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
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Mood disorders in Huntington's disease: from behavior to cellular and molecular mechanismsHuntingtin is critical both pre- and postsynaptically for long-term learning-related synaptic plasticity in AplysiaThe importance of integrating basic and clinical research toward the development of new therapies for Huntington diseaseNovel nuclear shuttle proteins, HDBP1 and HDBP2, bind to neuronal cell-specific cis-regulatory element in the promoter for the human Huntington's disease geneHuntingtin phosphorylation acts as a molecular switch for anterograde/retrograde transport in neuronspARIS-htt: an optimised expression platform to study huntingtin reveals functional domains required for vesicular traffickingHuntingtin has a membrane association signal that can modulate huntingtin aggregation, nuclear entry and toxicityClioquinol down-regulates mutant huntingtin expression in vitro and mitigates pathology in a Huntington's disease mouse model.Cystamine and cysteamine increase brain levels of BDNF in Huntington disease via HSJ1b and transglutaminase.Huntingtin in health and diseaseMetabolic dysfunction in Alzheimer's disease and related neurodegenerative disordersMultiple Aspects of Gene Dysregulation in Huntington's DiseaseTherapeutic potential of mood stabilizers lithium and valproic acid: beyond bipolar disorderHuman immunodeficiency virus type 1 alters brain-derived neurotrophic factor processing in neuronsmiR-210 links hypoxia with cell cycle regulation and is deleted in human epithelial ovarian cancerBrain-derived neurotrophic factorGlutamate and neurotrophic factors in neuronal plasticity and diseaseStimulation of NeuroD activity by huntingtin and huntingtin-associated proteins HAP1 and MLK2Asialoerythropoietin is not effective in the R6/2 line of Huntington's disease miceAssociation of Huntington's disease and schizophrenia-like psychosis in a Huntington's disease pedigree.The P42 peptide and Peptide-based therapies for Huntington's diseaseEpigenetics and Triplet-Repeat Neurological DiseasesNeurotrophic Factors and Their Potential Applications in Tissue Regeneration.Developing stem cell therapies for juvenile and adult-onset Huntington's diseaseDefining the role of the Bcl-2 family proteins in Huntington's diseaseHuntington's disease: the past, present, and future search for disease modifiers.Systems-Level G Protein-Coupled Receptor Therapy Across a Neurodegenerative Continuum by the GLP-1 Receptor SystemModeling Huntington's disease with induced pluripotent stem cellsMouse models of polyglutamine diseases in therapeutic approaches: review and data table. Part II.Therapeutic Approaches for Inhibition of Protein Aggregation in Huntington's DiseaseFingolimod for the treatment of neurological diseases-state of play and future perspectivesTranscriptional dysregulation in Huntington's disease: a failure of adaptive transcriptional homeostasisA huntingtin-mediated fast stress response halting endosomal trafficking is defective in Huntington's disease.Reinstating aberrant mTORC1 activity in Huntington's disease mice improves disease phenotypes.Amitriptyline improves motor function via enhanced neurotrophin signaling and mitochondrial functions in the murine N171-82Q Huntington disease model.Responses to environmental enrichment differ with sex and genotype in a transgenic mouse model of Huntington's diseaseA new drug design targeting the adenosinergic system for Huntington's diseaseMaintenance of basal levels of autophagy in Huntington's disease mouse models displaying metabolic dysfunctionPotential therapeutic effects of the MTOR inhibitors for preventing ageing and progeria-related disordersTransglutaminase 2 has opposing roles in the regulation of cellular functions as well as cell growth and death
P2860
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P2860
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
description
2001 nî lūn-bûn
@nan
2001 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2001 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
2001年の論文
@ja
2001年論文
@yue
2001年論文
@zh-hant
2001年論文
@zh-hk
2001年論文
@zh-mo
2001年論文
@zh-tw
2001年论文
@wuu
name
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@ast
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@en
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@nl
type
label
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@ast
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@en
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@nl
prefLabel
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@ast
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@en
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@nl
P2093
P50
P3181
P356
P1433
P1476
Loss of huntingtin-mediated BDNF gene transcription in Huntington's disease
@en
P2093
A Ciammola
B R Leavitt
D Goffredo
D Rigamonti
M E MacDonald
R M Friedlander
P304
P3181
P356
10.1126/SCIENCE.1059581
P407
P577
2001-06-14T00:00:00Z