Association of N-acetylgalactosamine-6-sulfate sulfatase with the multienzyme lysosomal complex of beta-galactosidase, cathepsin A, and neuraminidase. Possible implication for intralysosomal catabolism of keratan sulfate
about
Purification, cDNA cloning, and expression of a new human blood plasma glutamate carboxypeptidase homologous to N-acetyl-aspartyl-alpha-glutamate carboxypeptidase/prostate-specific membrane antigenMolecular mechanism of lysosomal sialidase deficiency in galactosialidosis involves its rapid degradationTransport of human lysosomal neuraminidase to mature lysosomes requires protective protein/cathepsin A.The Structure of Human GALNS Reveals the Molecular Basis for Mucopolysaccharidosis IV AMetabolism of vertebrate amino sugars with N-glycolyl groups: resistance of α2-8-linked N-glycolylneuraminic acid to enzymatic cleavageCo-Expression of NEU2 and GBA3 Causes a Drastic Reduction in Cytosolic Sialyl Free N-glycans in Human MKN45 Stomach Cancer Cells-Evidence for the Physical Interaction of NEU2 and GBA3Regulation of phagocytosis in macrophages by neuraminidase 1Lysosomal multienzyme complex: pros and cons of working togetherMutations in sialidosis impair sialidase binding to the lysosomal multienzyme complex.Splice donor site mutation in the lysosomal neuraminidase gene causing exon skipping and complete loss of enzyme activity in a sialidosis patient.Molecular testing of 163 patients with Morquio A (Mucopolysaccharidosis IVA) identifies 39 novel GALNS mutationsInhibition of CatA: an emerging strategy for the treatment of heart failure.Role of cathepsin A and lysosomes in the intracellular activation of novel antipapillomavirus agent GS-9191.Molecular mechanisms of pathogenesis in a glycosphingolipid and a glycoprotein storage diseaseStructural basis for substrate specificity of mammalian neuraminidases.Cell-permeable probe for identification and imaging of sialidasesGalactosialidosis: review and analysis of CTSA gene mutationsMucopolysaccharidosis IVA: correlation between genotype, phenotype and keratan sulfate levels.Mucopolysaccharidosis IVA and glycosaminoglycans.Identification of Selective Nanomolar Inhibitors of the Human Neuraminidase, NEU4Antibody against Microbial Neuraminidases Recognizes Human Sialidase 3 (NEU3): the Neuraminidase/Sialidase Superfamily Revisited.Lysosomal neuraminidase. Catalytic activation in insect cells is controlled by the protective protein/cathepsin A.Processing of lysosomal beta-galactosidase. The C-terminal precursor fragment is an essential domain of the mature enzyme.Glycan profiling of urine, amniotic fluid and ascitic fluid from galactosialidosis patients reveals novel oligosaccharides with reducing end hexose and aldohexonic acid residues.Porcine N-acetylgalactosamine 6-sulfatase (GALNS) cDNA sequence and expression in developing teeth.Saposin C is required for normal resistance of acid beta-glucosidase to proteolytic degradation.Altered gene expression in cells from patients with lysosomal storage disorders suggests impairment of the ubiquitin pathway.Aggrecan catabolism during mesenchymal stromal cellin vitrochondrogenesis
P2860
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P1343
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P2860
Association of N-acetylgalactosamine-6-sulfate sulfatase with the multienzyme lysosomal complex of beta-galactosidase, cathepsin A, and neuraminidase. Possible implication for intralysosomal catabolism of keratan sulfate
description
1996 nî lūn-bûn
@nan
1996 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
1996 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
1996年の論文
@ja
1996年論文
@yue
1996年論文
@zh-hant
1996年論文
@zh-hk
1996年論文
@zh-mo
1996年論文
@zh-tw
1996年论文
@wuu
name
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@ast
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@en
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@nl
type
label
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@ast
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@en
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@nl
prefLabel
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@ast
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@en
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@nl
P2860
P356
P1476
Association of N-acetylgalacto ...... catabolism of keratan sulfate
@en
P2093
A V Pshezhetsky
P2860
P304
P356
10.1074/JBC.271.45.28359
P407
P577
1996-11-08T00:00:00Z