Dysregulation of multiple facets of glycogen metabolism in a murine model of Pompe disease
about
Importance of tissue preparation methods in FTIR micro-spectroscopical analysis of biological tissues: 'traps for new users'Metabolomic Profiling of Pompe Disease-Induced Pluripotent Stem Cell-Derived Cardiomyocytes Reveals That Oxidative Stress Is Associated with Cardiac and Skeletal Muscle PathologyAntisense Oligonucleotide-mediated Suppression of Muscle Glycogen Synthase 1 Synthesis as an Approach for Substrate Reduction Therapy of Pompe DiseasePompe disease: literature review and case seriesPompe disease results in a Golgi-based glycosylation deficit in human induced pluripotent stem cell-derived cardiomyocytes.Lysosomal targeting strategies for design and delivery of bioactive for therapeutic interventions.13C/31P MRS Metabolic Biomarkers of Disease Progression and Response to AAV Delivery of hGAA in a Mouse Model of Pompe DiseaseAAV-mediated transcription factor EB (TFEB) gene delivery ameliorates muscle pathology and function in the murine model of Pompe Disease.
P2860
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P2860
Dysregulation of multiple facets of glycogen metabolism in a murine model of Pompe disease
description
2013 nî lūn-bûn
@nan
2013 թուականին հրատարակուած գիտական յօդուած
@hyw
2013 թվականին հրատարակված գիտական հոդված
@hy
2013年の論文
@ja
2013年論文
@yue
2013年論文
@zh-hant
2013年論文
@zh-hk
2013年論文
@zh-mo
2013年論文
@zh-tw
2013年论文
@wuu
name
Dysregulation of multiple face ...... murine model of Pompe disease
@ast
Dysregulation of multiple face ...... murine model of Pompe disease
@en
Dysregulation of multiple face ...... murine model of Pompe disease
@nl
type
label
Dysregulation of multiple face ...... murine model of Pompe disease
@ast
Dysregulation of multiple face ...... murine model of Pompe disease
@en
Dysregulation of multiple face ...... murine model of Pompe disease
@nl
prefLabel
Dysregulation of multiple face ...... murine model of Pompe disease
@ast
Dysregulation of multiple face ...... murine model of Pompe disease
@en
Dysregulation of multiple face ...... murine model of Pompe disease
@nl
P2093
P2860
P1433
P1476
Dysregulation of multiple face ...... murine model of Pompe disease
@en
P2093
Elizabeth Meyers
Kristin M Taylor
Michael Phipps
Priya S Kishnani
Rodney J Moreland
Ronald K Scheule
Seng H Cheng
P2860
P304
P356
10.1371/JOURNAL.PONE.0056181
P407
P577
2013-01-01T00:00:00Z