Retinal oxidation, apoptosis and age- and sex-differences in the mnd mutant mouse, a model of neuronal ceroid lipofuscinosis
about
A murine model of variant late infantile ceroid lipofuscinosis recapitulates behavioral and pathological phenotypes of human diseaseThe Batten disease gene CLN3 is required for the response to oxidative stress.Nitric oxide signaling is disrupted in the yeast model for Batten disease.Morphological characterization of the retinal degeneration in three strains of mice carrying the rd-3 mutation.Increased [³H]D-aspartate release and changes in glutamate receptor expression in the hippocampus of the mnd mouse.Galactolipid deficiency in the early pathogenesis of neuronal ceroid lipofuscinosis model Cln8mnd : implications to delayed myelination and oligodendrocyte maturation.
P2860
Retinal oxidation, apoptosis and age- and sex-differences in the mnd mutant mouse, a model of neuronal ceroid lipofuscinosis
description
2004 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2004 թվականի հուլիսին հրատարակված գիտական հոդված
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artículu científicu espublizáu en 2004
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im Juli 2004 veröffentlichter wissenschaftlicher Artikel
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scientific journal article
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vedecký článok (publikovaný 2004/07/16)
@sk
vědecký článek publikovaný v roce 2004
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wetenschappelijk artikel (gepubliceerd op 2004/07/16)
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наукова стаття, опублікована в липні 2004
@uk
مقالة علمية (نشرت في 16-7-2004)
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name
Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
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Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
@en
Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
@nl
type
label
Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
@ast
Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
@en
Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
@nl
prefLabel
Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
@ast
Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
@en
Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
@nl
P2093
P1433
P1476
Retinal oxidation, apoptosis a ...... neuronal ceroid lipofuscinosis
@en
P2093
Caterina Cascio
Domenica Russo
Giacoma Galizzi
Paolo Bigini
Patrizia Guarneri
Rosetta Guarneri
Stefania D'Agostino
Tiziana Mennini
P304
P356
10.1016/J.BRAINRES.2004.04.040
P407
P577
2004-07-16T00:00:00Z