Mitochondrial dysfunction in NnaD mutant flies and Purkinje cell degeneration mice reveals a role for Nna proteins in neuronal bioenergetics
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Recent advances in quantitative neuroproteomicsRedefining the cerebellar cortex as an assembly of non-uniform Purkinje cell microcircuitsAgeing, neuronal connectivity and brain disorders: an unsolved ripple effect.Alteration in 5-hydroxymethylcytosine-mediated epigenetic regulation leads to Purkinje cell vulnerability in ATM deficiency.Quantitative peptidomics of Purkinje cell degeneration micePurkinje cell degeneration in pcd mice reveals large scale chromatin reorganization and gene silencing linked to defective DNA repairA Drosophila model of the neurodegenerative disease SCA17 reveals a role of RBP-J/Su(H) in modulating the pathological outcome.Impaired Mitochondrial Energy Production Causes Light-Induced Photoreceptor Degeneration Independent of Oxidative Stress.Lack of Cytosolic Carboxypeptidase 1 Leads to Subfertility due to the Reduced Number of Antral Follicles in pcd3J-/- Females.Cytosolic carboxypeptidase 1 is involved in processing α- and β-tubulinMitochondrial Complex 1 Activity Measured by Spectrophotometry Is Reduced across All Brain Regions in Ageing and More Specifically in Neurodegeneration.A structural and functional analysis of Nna1 in Purkinje cell degeneration (pcd) mice.AFG3L2 supports mitochondrial protein synthesis and Purkinje cell survival.Reduction of mutant ataxin-7 expression restores motor function and prevents cerebellar synaptic reorganization in a conditional mouse model of SCA7Analysis of Mitochondrial haemoglobin in Parkinson's disease brain.A missense mutation in AGTPBP1 was identified in sheep with a lower motor neuron diseaseMitochondrial proteomic profiling reveals increased carbonic anhydrase II in aging and neurodegeneration.A mitochondrial location for haemoglobins--dynamic distribution in ageing and Parkinson's diseaseMitochondrial autophagy in neural function, neurodegenerative disease, neuron cell death, and aging.Functional genomics of the brain: uncovering networks in the CNS using a systems approach.Differential glial activation during the degeneration of Purkinje cells and mitral cells in the PCD mutant mice.Nucleolar disruption and cajal body disassembly are nuclear hallmarks of DNA damage-induced neurodegeneration in purkinje cells.Short-term succinic acid treatment mitigates cerebellar mitochondrial OXPHOS dysfunction, neurodegeneration and ataxia in a Purkinje-specific spinocerebellar ataxia type 1 (SCA1) mouse model.
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P2860
Mitochondrial dysfunction in NnaD mutant flies and Purkinje cell degeneration mice reveals a role for Nna proteins in neuronal bioenergetics
description
2010 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի հունիսին հրատարակված գիտական հոդված
@hy
artículu científicu espublizáu en 2010
@ast
im Juni 2010 veröffentlichter wissenschaftlicher Artikel
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scientific journal article
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vedecký článok (publikovaný 2010/06/24)
@sk
vědecký článek publikovaný v roce 2010
@cs
wetenschappelijk artikel (gepubliceerd op 2010/06/24)
@nl
наукова стаття, опублікована в червні 2010
@uk
مقالة علمية (نشرت في 24-6-2010)
@ar
name
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@ast
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@en
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@nl
type
label
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@ast
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@en
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@nl
prefLabel
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@ast
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@en
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@nl
P2093
P2860
P50
P921
P3181
P1433
P1476
Mitochondrial dysfunction in N ...... eins in neuronal bioenergetics
@en
P2093
Albert R La Spada
Amanda G Mason
Bryce L Sopher
Craig L Bennett
Gennifer Merrihew
Janice W Kansy
Jeremiah Eng
Leo J Pallanck
Lisa Chakrabarti
Parsa Kazemi-Esfarjani
P2860
P304
P3181
P356
10.1016/J.NEURON.2010.05.024
P407
P577
2010-06-01T00:00:00Z