Role of Stargardt-3 macular dystrophy protein (ELOVL4) in the biosynthesis of very long chain fatty acids
about
The role of ELOVL1 in very long-chain fatty acid homeostasis and X-linked adrenoleukodystrophyFunctional roles of bestrophins in ocular epitheliaBiosynthesis of polyunsaturated fatty acids in marine invertebrates: recent advances in molecular mechanismsBiology and therapy of inherited retinal degenerative disease: insights from mouse modelsLipid composition of the human eye: are red blood cells a good mirror of retinal and optic nerve fatty acids?Two modes of regulation of the fatty acid elongase ELOVL6 by the 3-ketoacyl-CoA reductase KAR in the fatty acid elongation cycleELOVL2 controls the level of n-6 28:5 and 30:5 fatty acids in testis, a prerequisite for male fertility and sperm maturation in miceSpecific sphingolipid content decrease in Cerkl knockdown mouse retinasRole and mechanism of the AMPK pathway in waterborne Zn exposure influencing the hepatic energy metabolism of Synechogobius hasta.Remodeling of retinal Fatty acids in an animal model of diabetes: a decrease in long-chain polyunsaturated fatty acids is associated with a decrease in fatty acid elongases Elovl2 and Elovl4.A role for ELOVL4 in the mouse meibomian gland and sebocyte cell biology.Regional changes in CNS and retinal glycerophospholipid profiles with age: a molecular blueprintPhospholipid meets all-trans-retinal: the making of RPE bisretinoidsDocosahexaenoic acid supplementation fully restores fertility and spermatogenesis in male delta-6 desaturase-null miceDistribution of ELOVL4 in the Developing and Adult Mouse Brain.Effect of reduced retinal VLC-PUFA on rod and cone photoreceptorsWhy has Nature Chosen Lutein and Zeaxanthin to Protect the Retina?Mutant ELOVL4 that causes autosomal dominant stargardt-3 macular dystrophy is misrouted to rod outer segment disksInner retina remodeling in a mouse model of stargardt-like macular dystrophy (STGD3).Examination of VLC-PUFA-deficient photoreceptor terminals.Retinal very long-chain PUFAs: new insights from studies on ELOVL4 proteinElovanoids are novel cell-specific lipid mediators necessary for neuroprotective signaling for photoreceptor cell integrityA monophasic extraction strategy for the simultaneous lipidome analysis of polar and nonpolar retina lipidsThe retinal pigment epithelium in health and diseaseLoss of lysophosphatidylcholine acyltransferase 1 leads to photoreceptor degeneration in rd11 mice.Comparative metabolomics reveals biogenesis of ascarosides, a modular library of small-molecule signals in C. elegans.Retinal sphingolipids and their very-long-chain fatty acid-containing species.Defective lipid transport and biosynthesis in recessive and dominant Stargardt macular degenerationLong-chain and very long-chain polyunsaturated fatty acids in ocular aging and age-related macular degenerationChemical synthesis of deuterium-labeled and unlabeled very long chain polyunsaturated fatty acidsRole of long-chain and very-long-chain polyunsaturated fatty acids in macular degenerations and dystrophiesGenetics and molecular pathology of Stargardt-like macular degeneration.Cooperative Synthesis of Ultra Long-Chain Fatty Acid and Ceramide during Keratinocyte Differentiation.Epidermal expression of an Elovl4 transgene rescues neonatal lethality of homozygous Stargardt disease-3 mice.A novel recessive mutation in the gene ELOVL4 causes a neuro-ichthyotic disorder with variable expressivity.Role of Elovl4 protein in the biosynthesis of docosahexaenoic acidAdiponectin receptor 1 conserves docosahexaenoic acid and promotes photoreceptor cell survival.Liquid chromatography-high resolution mass spectrometry analysis of fatty acid metabolism.Association of n3 and n6 polyunsaturated fatty acids in red blood cell membrane and plasma with severity of normal tension glaucoma.ELOVL4 protein preferentially elongates 20:5n3 to very long chain PUFAs over 20:4n6 and 22:6n3
P2860
Q24300003-DBDF933F-ADBA-4EBC-8682-29ED16388B2DQ24657568-7A0BA73A-D72D-4460-B99F-9275A5239651Q27006849-AD050742-FB64-4816-9CEE-9EA704539D71Q28084726-5784C914-2A4C-4C2A-A81F-DF5F3625ECE1Q28482205-DF0E0C38-D407-445B-A544-9AB4AD16EE0CQ28540503-E6607350-ABC8-41E9-8BE9-9F37B057012AQ28591687-C3FCDA40-2BFE-4B37-A98E-7B9C74A1F446Q28594039-F11A388C-2FFC-46EB-8A92-7CA1154FC111Q30379916-74AF5DB0-6C97-4F7D-8439-861AAA6A63E8Q33556542-15300F5D-D649-4733-85B0-0D971561DD6AQ33558508-57A7F646-0102-45C5-B28E-1CD2C1004878Q33567994-B7AB8C59-FC5A-4E70-805E-B839B7C40838Q33577803-D426A643-C1DE-4CC5-836F-C001F0CCCDE3Q33577857-0D0417DF-1893-418E-A6AA-D38C1089DB22Q33619349-230284EE-B98F-40C9-A5C6-DE61716B9776Q33636596-66A92913-C509-420A-8500-2C9BA48043EAQ33687586-993D37FD-1EAD-4943-AD19-A6C868CA3CCFQ33761007-68EEFAC0-F9F3-4573-9157-AC0A07D44BFDQ33844987-7206626E-47E8-49D6-89EE-28079C304FF9Q33852881-DC53140C-84FE-4E17-9D33-5D91B14378D3Q33902007-110EBC6B-C9DF-4CE1-811F-F2DF2793B1A0Q33902944-6D2ED88D-832F-43A7-BA47-DF3067EF2D79Q33945138-47EA592F-B6BB-4A2F-B24C-42655295FB89Q33998365-1CE01A83-4A55-4212-9E87-006FA8A3B5B3Q34100261-F0289C68-DA33-40D3-BF43-5D64135EE45EQ34125569-74232D3D-B241-4169-8833-0404D068C62BQ34135588-82B1F05C-7C6D-466C-9DA5-07735A86D1F5Q34157723-9B22DDBD-EB3B-4DDE-8D1B-146F3C483BDAQ34188018-31A45EEC-7087-4804-893F-8BCC7B8BA10AQ34291817-9EA17A79-5A9C-4026-BB0A-1061B1DFBAEBQ34334822-FCDB4B6C-09E5-4F6B-98B9-CECA2BF30C3FQ34691651-008F684C-D1F8-4682-9ECA-9E2488C05F0FQ34796919-93F745BD-0E75-40A6-9FB0-FC62C10FA3B0Q34955833-D2FC7D85-8A7A-497D-974A-5C23FA445E9EQ35103230-062072D6-6468-4742-ADF6-800A790232A5Q35150420-F8C6DE08-984D-43C2-B4ED-FB47984F043BQ35154046-864BB5E9-7822-4EEE-9306-3564EAA5FDA2Q35593211-A7CAA00B-EE54-41FB-9ECC-D734924BDCD7Q35691894-5FAFEBAC-22E1-4209-AA60-164F2FF330E3Q35747790-74288F34-2575-4110-ADBE-B4ACC4E3D9FA
P2860
Role of Stargardt-3 macular dystrophy protein (ELOVL4) in the biosynthesis of very long chain fatty acids
description
2008 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
article publié dans les Procee ...... f the United States of America
@fr
artículu científicu espublizáu en 2008
@ast
im September 2008 veröffentlichter wissenschaftlicher Artikel
@de
scientific journal article
@en
vedecký článok (publikovaný 2008/09/02)
@sk
vědecký článek publikovaný v roce 2008
@cs
wetenschappelijk artikel (gepubliceerd op 2008/09/02)
@nl
наукова стаття, опублікована у вересні 2008
@uk
name
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@ast
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@en
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@nl
type
label
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@ast
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@en
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@nl
prefLabel
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@ast
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@en
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@nl
P2093
P2860
P3181
P356
P1476
Role of Stargardt-3 macular dy ...... of very long chain fatty acids
@en
P2093
Kimberly Henry
Martin-Paul Agbaga
Md Nawajes A. Mandal
Michael H. Elliott
Richard S. Brush
Robert E. Anderson
P2860
P304
12843–12848
P3181
P356
10.1073/PNAS.0802607105
P407
P577
2008-09-02T00:00:00Z