Nuclear lamins: laminopathies and their role in premature ageing.
about
Lamin A/C haploinsufficiency modulates the differentiation potential of mouse embryonic stem cellsSumoylation regulates lamin A function and is lost in lamin A mutants associated with familial cardiomyopathiesA novel homozygous p.Arg527Leu LMNA mutation in two unrelated Egyptian families causes overlapping mandibuloacral dysplasia and progeria syndromeLamin A-dependent misregulation of adult stem cells associated with accelerated ageingIntroducing intermediate filaments: from discovery to diseaseA Review of the Giant Protein Titin in Clinical Molecular Diagnostics of CardiomyopathiesMolecular insights into the premature aging disease progeriaSorting nexin 6 enhances lamin a synthesis and incorporation into the nuclear envelopeIn silico synchronization reveals regulators of nuclear ruptures in lamin A/C deficient model cells.Crystal structures of the coil 2B fragment and the globular tail domain of human lamin B1Heading in the Right Direction: Understanding Cellular Orientation Responses to Complex Biophysical EnvironmentsImplications and Assessment of the Elastic Behavior of Lamins in LaminopathiesThe cell biology of agingPrelamin A farnesylation and progeroid syndromesDeficient expression of aldehyde dehydrogenase 1A1 is consistent with increased sensitivity of Gorlin syndrome patients to radiation carcinogenesisSuppression of lamin A/C by short hairpin RNAs promotes adipocyte lineage commitment in mesenchymal progenitor cell line, ROB-C26Molecular image analysis: quantitative description and classification of the nuclear lamina in human mesenchymal stem cellsRoutine phasing of coiled-coil protein crystal structures with AMPLEEvolution of the lamin protein family: what introns can tell.The defective nuclear lamina in Hutchinson-gilford progeria syndrome disrupts the nucleocytoplasmic Ran gradient and inhibits nuclear localization of Ubc9.Pathological features in the LmnaDhe/+ mutant mouse provide a novel model of human otitis media and laminopathies.Alterations in mitosis and cell cycle progression caused by a mutant lamin A known to accelerate human agingLamin B1 mediates cell-autonomous neuropathology in a leukodystrophy mouse model.Nuclear envelope lamin-A couples actin dynamics with immunological synapse architecture and T cell activation.Barrier-to-autointegration factor proteome reveals chromatin-regulatory partners.Characterization of lamin mutation phenotypes in Drosophila and comparison to human laminopathies.Lamin A/C is a risk biomarker in colorectal cancer.Lamin A rod domain mutants target heterochromatin protein 1alpha and beta for proteasomal degradation by activation of F-box protein, FBXW10Human adult stem cells as the target cells for the initiation of carcinogenesis and for the generation of "cancer stem cells".Specifying peripheral heterochromatin during nuclear lamina reassembly.Nuclear localization signal deletion mutants of lamin A and progerin reveal insights into lamin A processing and emerin targetingShear stress-induced mechanotransduction protein deregulation and vasculopathy in a mouse model of progeria.Lamin-binding ProteinsDNA damage and laminsImpact of farnesylation inhibitors on survival in Hutchinson-Gilford progeria syndrome.Loss of lamin B1 results in prolongation of S phase and decondensation of chromosome territoriesStabilization of the spectrin-like domains of nesprin-1α by the evolutionarily conserved "adaptive" domain.Conserved cysteine residues in the mammalian lamin A tail are essential for cellular responses to ROS generation.Clinical trial of a farnesyltransferase inhibitor in children with Hutchinson-Gilford progeria syndrome.Nuclear lamins and neurobiology.
P2860
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P2860
Nuclear lamins: laminopathies and their role in premature ageing.
description
2006 nî lūn-bûn
@nan
2006 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
Nuclear lamins: laminopathies and their role in premature ageing.
@ast
Nuclear lamins: laminopathies and their role in premature ageing.
@en
type
label
Nuclear lamins: laminopathies and their role in premature ageing.
@ast
Nuclear lamins: laminopathies and their role in premature ageing.
@en
prefLabel
Nuclear lamins: laminopathies and their role in premature ageing.
@ast
Nuclear lamins: laminopathies and their role in premature ageing.
@en
P2093
P1476
Nuclear lamins: laminopathies and their role in premature ageing
@en
P2093
C J Hutchison
F C S Ramaekers
J L V Broers
R Ben Yaou
P304
P356
10.1152/PHYSREV.00047.2005
P50
P577
2006-07-01T00:00:00Z