The atomic model of the human protective protein/cathepsin A suggests a structural basis for galactosialidosis.
about
Proteolytic Activation of Human Cathepsin AStable expression of protective protein/cathepsin A-green fluorescent protein fusion genes in a fibroblastic cell line from a galactosialidosis patient. Model system for revealing the intracellular transport of normal and mutated lysosomal enzymes.Mutations in sialidosis impair sialidase binding to the lysosomal multienzyme complex.Galactosialidosis: review and analysis of CTSA gene mutationsHeterodimerization of the sialidase NEU1 with the chaperone protective protein/cathepsin A prevents its premature oligomerization.Galactosialidosis: historic aspects and overview of investigated and emerging treatment options.Turning the backbone into an ankylosed concrete-like structure: Case report.
P2860
Q27682025-E864DF46-B2F5-4FEA-9814-90189F1896A0Q30631709-173F7E72-7173-4226-A1F1-2B54813BD2D0Q33940580-C0A7A6C0-C712-407B-9B4F-9CAE8EA3295AQ37079230-B0724621-6C5E-4DE0-9F2C-3A6ADB5684FEQ37460020-B83CE556-D57E-488B-BE56-0BF5F64BC838Q38672166-B59A4180-15FD-4B00-B6BA-B38A10F66DD1Q52593863-228F612C-4A43-4BC9-B2A8-EAE029BFAE15
P2860
The atomic model of the human protective protein/cathepsin A suggests a structural basis for galactosialidosis.
description
1998 nî lūn-bûn
@nan
1998 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
1998 թվականի հունվարին հրատարակված գիտական հոդված
@hy
1998年の論文
@ja
1998年論文
@yue
1998年論文
@zh-hant
1998年論文
@zh-hk
1998年論文
@zh-mo
1998年論文
@zh-tw
1998年论文
@wuu
name
The atomic model of the human ...... l basis for galactosialidosis.
@ast
The atomic model of the human ...... l basis for galactosialidosis.
@en
type
label
The atomic model of the human ...... l basis for galactosialidosis.
@ast
The atomic model of the human ...... l basis for galactosialidosis.
@en
prefLabel
The atomic model of the human ...... l basis for galactosialidosis.
@ast
The atomic model of the human ...... l basis for galactosialidosis.
@en
P2093
P2860
P356
P1476
The atomic model of the human ...... l basis for galactosialidosis.
@en
P2093
P2860
P304
P356
10.1073/PNAS.95.2.621
P407
P577
1998-01-01T00:00:00Z