Direct interaction of the spinal muscular atrophy disease protein SMN with the small nucleolar RNA-associated protein fibrillarin.
about
Purification of native survival of motor neurons complexes and identification of Gemin6 as a novel componentIdentification and characterization of Gemin7, a novel component of the survival of motor neuron complexStepwise RNP assembly at the site of H/ACA RNA transcription in human cellsMammalian and yeast U3 snoRNPs are matured in specific and related nuclear compartments.Numerous microRNPs in neuronal cells containing novel microRNAsmiRNPs: a novel class of ribonucleoproteins containing numerous microRNAsSMN, the spinal muscular atrophy protein, forms a pre-import snRNP complex with snurportin1 and importin betaELL and EAF1 are Cajal body components that are disrupted in MLL-ELL leukemiaMalignant brain tumor repeats: a three-leaved propeller architecture with ligand/peptide binding pocketsNaf1p, an essential nucleoplasmic factor specifically required for accumulation of box H/ACA small nucleolar RNPsNaf1 p is a box H/ACA snoRNP assembly factorDeterminants of the interaction of the spinal muscular atrophy disease protein SMN with the dimethylarginine-modified box H/ACA small nucleolar ribonucleoprotein GAR1Human fibrillarin forms a sub-complex with splicing factor 2-associated p32, protein arginine methyltransferases, and tubulins alpha 3 and beta 1 that is independent of its association with preribosomal ribonucleoprotein complexesA novel WD repeat protein component of the methylosome binds Sm proteinsProlactin increases SMN expression and survival in a mouse model of severe spinal muscular atrophy via the STAT5 pathway.The SMN complex: an assembly machine for RNPsFibrillarin is essential for early development and required for accumulation of an intron-encoded small nucleolar RNA in the mouseMolecular determinants of survival motor neuron (SMN) protein cleavage by the calcium-activated protease, calpainLymphotropic Herpesvirus saimiri uses the SMN complex to assemble Sm cores on its small RNAs.Spinal muscular atrophy: why do low levels of survival motor neuron protein make motor neurons sick?The product of the survival of motor neuron (SMN) gene is a human telomerase-associated protein.Sequence-specific interaction of U1 snRNA with the SMN complexSpecific sequence features, recognized by the SMN complex, identify snRNAs and determine their fate as snRNPsTudor domains bind symmetrical dimethylated arginines.Small nucleolar RNAs: versatile trans-acting molecules of ancient evolutionary origin.Fishing for a mechanism: using zebrafish to understand spinal muscular atrophy.Spinal muscular atrophy: recent advances and future prospects.p38 Mitogen-activated protein kinase stabilizes SMN mRNA through RNA binding protein HuR.The many facets of H/ACA ribonucleoproteinsIn vivo kinetics of Cajal body componentsMolecular and cellular basis of spinal muscular atrophy.Cajal body proteins differentially affect the processing of box C/D scaRNPs.Interaction of a plant virus-encoded protein with the major nucleolar protein fibrillarin is required for systemic virus infectionA transgene carrying an A2G missense mutation in the SMN gene modulates phenotypic severity in mice with severe (type I) spinal muscular atrophy.Implication of the SMN complex in the biogenesis and steady state level of the signal recognition particle.Identification of genes that function in the biogenesis and localization of small nucleolar RNAs in Saccharomyces cerevisiae.Biogenesis and intranuclear trafficking of human box C/D and H/ACA RNPs.Molecular functions of the SMN complex.snRNAs contain specific SMN-binding domains that are essential for snRNP assemblySpinal muscular atrophy and a model for survival of motor neuron protein function in axonal ribonucleoprotein complexes
P2860
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P2860
Direct interaction of the spinal muscular atrophy disease protein SMN with the small nucleolar RNA-associated protein fibrillarin.
description
2001 nî lūn-bûn
@nan
2001 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
2001 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
2001年の論文
@ja
2001年論文
@yue
2001年論文
@zh-hant
2001年論文
@zh-hk
2001年論文
@zh-mo
2001年論文
@zh-tw
2001年论文
@wuu
name
Direct interaction of the spin ...... ssociated protein fibrillarin.
@ast
Direct interaction of the spin ...... ssociated protein fibrillarin.
@en
type
label
Direct interaction of the spin ...... ssociated protein fibrillarin.
@ast
Direct interaction of the spin ...... ssociated protein fibrillarin.
@en
prefLabel
Direct interaction of the spin ...... ssociated protein fibrillarin.
@ast
Direct interaction of the spin ...... ssociated protein fibrillarin.
@en
P2093
P2860
P356
P1476
Direct interaction of the spin ...... ssociated protein fibrillarin.
@en
P2093
Badbanchi F
Gorzynski K
P2860
P304
38645-38651
P356
10.1074/JBC.M106161200
P407
P577
2001-08-16T00:00:00Z