Purification of native survival of motor neurons complexes and identification of Gemin6 as a novel component
about
Identification and characterization of Gemin7, a novel component of the survival of motor neuron complexGemin8 is a novel component of the survival motor neuron complex and functions in small nuclear ribonucleoprotein assemblyGemin8 is required for the architecture and function of the survival motor neuron complexIsolation and characterization of post-splicing lariat-intron complexesStructure of a key intermediate of the SMN complex reveals Gemin2's crucial function in snRNP assemblyNumerous microRNPs in neuronal cells containing novel microRNAsHigh expression level of Tra2-β1 is responsible for increased SMN2 exon 7 inclusion in the testis of SMA miceA motor function for the DEAD-box RNA helicase, Gemin3, in DrosophilaFunctional mammalian spliceosomal complex E contains SMN complex proteins in addition to U1 and U2 snRNPs.Naf1 p is a box H/ACA snoRNP assembly factorGemin5 delivers snRNA precursors to the SMN complex for snRNP biogenesisIn vitro and in cellulo evidences for association of the survival of motor neuron complex with the fragile X mental retardation proteinGemin5-snRNA interaction reveals an RNA binding function for WD repeat domainsThe RNA-binding protein Gemin5 binds directly to the ribosome and regulates global translationSMN-independent subunits of the SMN complex. Identification of a small nuclear ribonucleoprotein assembly intermediateUnrip is a component of SMN complexes active in snRNP assemblyThe SMN complex: an assembly machine for RNPsA role for SMN exon 7 splicing in the selective vulnerability of motor neurons in spinal muscular atrophySMN in spinal muscular atrophy and snRNP biogenesisMolecular determinants of survival motor neuron (SMN) protein cleavage by the calcium-activated protease, calpainLymphotropic Herpesvirus saimiri uses the SMN complex to assemble Sm cores on its small RNAs.The role of nuclear bodies in gene expression and disease.Sequence-specific interaction of U1 snRNA with the SMN complexGene targeting of Gemin2 in mice reveals a correlation between defects in the biogenesis of U snRNPs and motoneuron cell death.Specific sequence features, recognized by the SMN complex, identify snRNAs and determine their fate as snRNPsThe SMN complex is associated with snRNPs throughout their cytoplasmic assembly pathwayAbnormal interaction of motor neuropathy-associated mutant HspB8 (Hsp22) forms with the RNA helicase Ddx20 (gemin3).Functional association of the Microprocessor complex with the spliceosome.The Gemin associates of survival motor neuron are required for motor function in Drosophila.Molecular and cellular basis of spinal muscular atrophy.Expression of Muscle-Specific MiRNA 206 in the Progression of Disease in a Murine SMA ModelInhibition of U snRNP assembly by a virus-encoded proteinaseReconstitution of the human U snRNP assembly machinery reveals stepwise Sm protein organizationNUFIP and the HSP90/R2TP chaperone bind the SMN complex and facilitate assembly of U4-specific proteins.Implication of the SMN complex in the biogenesis and steady state level of the signal recognition particle.Pre-mRNA splicing and retinitis pigmentosaIdentification and characterisation of a nuclear localisation signal in the SMN associated protein, Gemin4.SMN deficiency causes tissue-specific perturbations in the repertoire of snRNAs and widespread defects in splicing.Identification and characterization of the porcine (Sus scrofa) survival motor neuron (SMN1) gene: an animal model for therapeutic studiesMolecular functions of the SMN complex.
P2860
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P2860
Purification of native survival of motor neurons complexes and identification of Gemin6 as a novel component
description
2002 nî lūn-bûn
@nan
2002 թուականի Մարտին հրատարակուած գիտական յօդուած
@hyw
2002 թվականի մարտին հրատարակված գիտական հոդված
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2002年の論文
@ja
2002年学术文章
@wuu
2002年学术文章
@zh-cn
2002年学术文章
@zh-hans
2002年学术文章
@zh-my
2002年学术文章
@zh-sg
2002年學術文章
@yue
name
Purification of native surviva ...... of Gemin6 as a novel component
@ast
Purification of native surviva ...... of Gemin6 as a novel component
@en
Purification of native surviva ...... of Gemin6 as a novel component
@en-gb
Purification of native surviva ...... of Gemin6 as a novel component
@nl
type
label
Purification of native surviva ...... of Gemin6 as a novel component
@ast
Purification of native surviva ...... of Gemin6 as a novel component
@en
Purification of native surviva ...... of Gemin6 as a novel component
@en-gb
Purification of native surviva ...... of Gemin6 as a novel component
@nl
prefLabel
Purification of native surviva ...... of Gemin6 as a novel component
@ast
Purification of native surviva ...... of Gemin6 as a novel component
@en
Purification of native surviva ...... of Gemin6 as a novel component
@en-gb
Purification of native surviva ...... of Gemin6 as a novel component
@nl
P2093
P2860
P3181
P356
P1476
Purification of native surviva ...... of Gemin6 as a novel component
@en
P2093
Gideon Dreyfuss
Jennifer Baccon
Matthias Mann
P2860
P304
P3181
P356
10.1074/JBC.M110141200
P407
P577
2002-03-01T00:00:00Z