Co-chaperone CHIP stabilizes aggregate-prone malin, a ubiquitin ligase mutated in Lafora disease.
about
Lafora progressive myoclonus epilepsy: NHLRC1 mutations affect glycogen metabolismA Decade of Boon or Burden: What Has the CHIP Ever Done for Cellular Protein Quality Control Mechanism Implicated in Neurodegeneration and Aging?Identification of CHIP as a novel causative gene for autosomal recessive cerebellar ataxiaAncient origin of animal U-box ubiquitin ligases.The laforin-malin complex, involved in Lafora disease, promotes the incorporation of K63-linked ubiquitin chains into AMP-activated protein kinase beta subunits.Increased oxidative stress and impaired antioxidant response in Lafora disease.Dimerization of the glucan phosphatase laforin requires the participation of cysteine 329.Malin regulates Wnt signaling pathway through degradation of dishevelled2Laforin, a protein with many faces: glucan phosphatase, adapter protein, et alii.Serine/threonine protein phosphatase 5 (PP5) interacts with substrate under heat stress conditions and forms protein complex in Arabidopsis.Dysfunction of the ubiquitin ligase Ube3a may be associated with synaptic pathophysiology in a mouse model of Huntington diseaseDeciphering the role of malin in the lafora progressive myoclonus epilepsyNeuronatin-mediated aberrant calcium signaling and endoplasmic reticulum stress underlie neuropathology in Lafora diseaseDoxorubicin attenuates CHIP-guarded HSF1 nuclear translocation and protein stability to trigger IGF-IIR-dependent cardiomyocyte death.Phenotype variations in Lafora progressive myoclonus epilepsy: possible involvement of genetic modifiers?Emerging role of autophagy in pediatric neurodegenerative and neurometabolic diseases.Inflammation in Lafora Disease: Evolution with Disease Progression in Laforin and Malin Knock-out Mouse Models.Deficiency of Ube3a in Huntington's disease mice brain increases aggregate load and accelerates disease pathology.Reversal of reduced parvalbumin neurons in hippocampus and amygdala of Angelman syndrome model mice by chronic treatment of fluoxetine.Environmental Enrichment Improves Behavioral Abnormalities in a Mouse Model of Angelman Syndrome.
P2860
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P2860
Co-chaperone CHIP stabilizes aggregate-prone malin, a ubiquitin ligase mutated in Lafora disease.
description
2009 nî lūn-bûn
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2009 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2009 թվականի նոյեմբերին հրատարակված գիտական հոդված
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2009年の論文
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2009年学术文章
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2009年学术文章
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2009年学术文章
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2009年学术文章
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2009年学术文章
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2009年學術文章
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name
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@ast
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@en
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@nl
type
label
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@ast
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@en
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@nl
prefLabel
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@ast
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@en
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@nl
P2860
P356
P1476
Co-chaperone CHIP stabilizes a ...... ase mutated in Lafora disease.
@en
P2093
Jaiprakash Sharma
Ranjan Maity
P2860
P304
P356
10.1074/JBC.M109.006312
P407
P577
2009-11-05T00:00:00Z