Upregulation of elastase activity in aorta in mucopolysaccharidosis I and VII dogs may be due to increased cytokine expression.
about
Effects of enzyme replacement therapy started late in a murine model of mucopolysaccharidosis type IImmune-Mediated Inflammation May Contribute to the Pathogenesis of Cardiovascular Disease in Mucopolysaccharidosis Type IAortic Root Dilatation in Mucopolysaccharidosis I-VIIThe effect of neonatal gene therapy on skeletal manifestations in mucopolysaccharidosis VII dogs after a decade.Arterial pathology in canine mucopolysaccharidosis-I and response to therapyCardiac disease in patients with mucopolysaccharidosis: presentation, diagnosis and managementPathogenesis of aortic dilatation in mucopolysaccharidosis VII mice may involve complement activation.Excessive activity of cathepsin K is associated with cartilage defects in a zebrafish model of mucolipidosis II.A review of gene therapy in canine and feline models of lysosomal storage disorders.Pathogenesis of lumbar spine disease in mucopolysaccharidosis VII.Effect of neonatal gene therapy on lumbar spine disease in mucopolysaccharidosis VII dogsNeonatal cellular and gene therapies for mucopolysaccharidoses: the earlier the better?Pathogenesis of mitral valve disease in mucopolysaccharidosis VII dogs.The effect of neonatal gene therapy with a gamma retroviral vector on cardiac valve disease in mucopolysaccharidosis VII dogs after a decadeCarotid intima-media thickness is increased in patients with treated mucopolysaccharidosis types I and II, and correlates with arterial stiffness.Hyaluronan, a crucial regulator of inflammation.The Carotid Intima-Media Thickness and Arterial Stiffness of Pediatric Mucopolysaccharidosis Patients Are Increased Compared to Both Pediatric and Adult ControlsCurrent and emerging management options for patients with Morquio A syndromeExtracellular matrix components: an intricate network of possible biomarkers for lysosomal storage disorders?Prolonged Expression of Secreted Enzymes in Dogs After Liver-Directed Delivery of Sleeping Beauty Transposons: Implications for Non-Viral Gene Therapy of Systemic Disease.Cardiovascular Histopathology of a 11-Year Old with Mucopolysaccharidosis VII Demonstrates Fibrosis, Macrophage Infiltration, and Arterial Luminal Stenosis.Unfolded protein response is not activated in the mucopolysaccharidoses but protein disulfide isomerase 5 is deregulated.
P2860
Q27316418-76F05CCB-4DD0-4F2F-B05C-94490B6A637FQ27318642-2648DBA3-B006-41DB-B246-3FF6EB703020Q30367116-BE2E9B42-89E7-434E-A2FE-AAAC16811081Q30540876-A73BF33F-DF84-4A6C-92C1-2C87629389E4Q34883690-5D25DEED-D83B-4DFC-AE31-B5FAC9100170Q35587435-091879BC-7D42-4699-886C-00E3177905B2Q35767677-0487A344-A329-43A9-8E08-3E0B7241D20CQ35794555-B2208334-EE98-4D59-B585-9ACE825E204DQ35894676-6093F4BA-E791-4F37-B68F-27599D962DD4Q36190865-698AAA8D-3C45-4EB0-BA19-5AE02061123CQ36195519-C05BB182-286A-4713-BF2E-8E4246E6A356Q36582259-0A9B2A04-47E0-4DFE-8CFF-16B6A42DB47AQ37238697-783C3DAC-2B9E-4B52-81EF-8C9154D6B9D3Q37238895-112C80A9-0385-43EB-8069-56041CF48340Q37624919-2EF4BAB3-3EF9-4874-AD90-A352E01105DEQ37629440-5A39DF67-7087-4C92-AD0B-66C26E4A504BQ37729304-65551706-8177-4212-8CBD-AEF873F0DD01Q38081868-2D4AA895-9C48-490E-8730-6C985FAE83B4Q38085972-A13F3A07-B64D-44CA-A7BF-83328E97F386Q40191364-545AB470-ED3B-44C5-80AF-8353A0E74E03Q44075433-3925DC55-C640-4DC3-ACCC-7F1EE9E07EA7Q48835669-AF865449-35BC-466D-B6D1-1F6F47EC1747
P2860
Upregulation of elastase activity in aorta in mucopolysaccharidosis I and VII dogs may be due to increased cytokine expression.
description
2009 nî lūn-bûn
@nan
2009 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2009 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2009年の論文
@ja
2009年論文
@yue
2009年論文
@zh-hant
2009年論文
@zh-hk
2009年論文
@zh-mo
2009年論文
@zh-tw
2009年论文
@wuu
name
Upregulation of elastase activ ...... increased cytokine expression.
@ast
Upregulation of elastase activ ...... increased cytokine expression.
@en
type
label
Upregulation of elastase activ ...... increased cytokine expression.
@ast
Upregulation of elastase activ ...... increased cytokine expression.
@en
prefLabel
Upregulation of elastase activ ...... increased cytokine expression.
@ast
Upregulation of elastase activ ...... increased cytokine expression.
@en
P2093
P2860
P1476
Upregulation of elastase activ ...... increased cytokine expression.
@en
P2093
Bruce Linders
Jason A Metcalf
Katherine P Ponder
Mark Haskins
Meg M Sleeper
Michael P Whyte
Patricia O'Donnell
P2860
P304
P356
10.1016/J.YMGME.2009.12.003
P577
2009-12-11T00:00:00Z