Epithelial stress and apoptosis underlie Hermansky-Pudlak syndrome-associated interstitial pneumonia
about
Genetic interstitial lung diseaseDysregulation of galectin-3. Implications for Hermansky-Pudlak syndrome pulmonary fibrosis.Pathogenesis of idiopathic pulmonary fibrosis: review of recent findings.Early alveolar epithelial dysfunction promotes lung inflammation in a mouse model of Hermansky-Pudlak syndrome.Interstitial lung disease and pulmonary fibrosis in Hermansky-Pudlak syndrome type 2, an adaptor protein-3 complex diseaseChitinase 3-like-1 and its receptors in Hermansky-Pudlak syndrome-associated lung disease.Genetic studies provide clues on the pathogenesis of idiopathic pulmonary fibrosis.The alveolar epithelium determines susceptibility to lung fibrosis in Hermansky-Pudlak syndrome.Pirfenidone for the treatment of Hermansky-Pudlak syndrome pulmonary fibrosisMAP1LC3B overexpression protects against Hermansky-Pudlak syndrome type-1-induced defective autophagy in vitroEpithelial-macrophage interactions determine pulmonary fibrosis susceptibility in Hermansky-Pudlak syndrome.Grainyhead-like 2 (GRHL2) distribution reveals novel pathophysiological differences between human idiopathic pulmonary fibrosis and mouse models of pulmonary fibrosis.Update in diffuse parenchymal lung disease 2010.The role of dimethylarginine dimethylaminohydrolase (DDAH) in pulmonary fibrosis.Abca3 haploinsufficiency is a risk factor for lung injury induced by hyperoxia or mechanical ventilation in a murine model.Altered surfactant homeostasis and alveolar epithelial cell stress in amiodarone-induced lung fibrosis.Tissue remodelling in pulmonary fibrosis.Endoplasmic reticulum stress mediates house dust mite-induced airway epithelial apoptosis and fibrosis.Secretome of human bronchial epithelial cells in response to the fungal pathogen Aspergillus fumigatus analyzed by differential in-gel electrophoresis.Regulation of macroautophagy in amiodarone-induced pulmonary fibrosis.Multiple ways to die: delineation of the unfolded protein response and apoptosis induced by Surfactant Protein C BRICHOS mutantsHermansky-Pudlak syndrome type 4 with interstitial pneumonia.Pulmonary Fibrosis in Hermansky-Pudlak Syndrome.Hermansky-Pudlak syndrome interstitial pneumonia: it's the epithelium, stupid!Interleukin-1 promotes coagulation, which is necessary for protective immunity in the lung against Streptococcus pneumoniae infection.Insights from human genetic studies of lung and organ fibrosis.Gene-edited MLE-15 Cells as a Model for the Hermansky Pudlak Syndromes.An Official American Thoracic Society Workshop Report: Translational Research in Rare Respiratory Diseases.Surfactant replacement therapy reduces acute lung injury and collapse induration-related lung remodeling in the bleomycin model.Interaction of macrophages with apoptotic cells inhibits transdifferentiation and invasion of lung fibroblasts.Hermansky-Pudlak Syndrome.Linking progression of fibrotic lung remodeling and ultrastructural alterations of alveolar epithelial type II cells in the amiodarone mouse model.Hermansky-Pudlak syndrome type 2 manifests with fibrosing lung disease early in childhood.
P2860
Q24626239-55A4C66E-7CF7-4583-8C34-BF3A5D02290FQ33799623-973BFCB5-078D-486E-B55B-870B7B02CF6AQ34019921-1035A210-8A5A-458E-AC69-142F2000B5F8Q35219750-4744FBFA-1576-4799-AC5C-A066F3BE74C0Q35718958-1DB0B32D-83B5-4592-96EE-CBA463731DD6Q36040475-E015096D-6005-4A01-A7CD-E9248068286BQ36485998-E13B6C41-8A17-4708-B194-4A4626B935A8Q36488735-726946E9-4662-413F-BFCC-FAF4B6861C92Q36850698-63EDCFDC-36A0-4806-B650-092EBF9DAEA1Q36955310-7A3F8622-1E7B-45C4-8BD5-67D6ACAD874BQ37351580-22E9C18E-B9D5-45AD-A28D-7D04D3164DD3Q37629230-3C1690BC-41B9-4AD6-ACEF-7CBCD26F7D0FQ37877430-61687205-5FD7-44ED-AD77-5D484F5E0113Q38055449-E0F196B4-66A0-42BD-A363-3D1320CDC11AQ38313892-A7F01484-4D4D-4429-B610-29584D3E855DQ38962370-D6CCCDD7-FB3C-480F-8CC1-F4473D53AC6AQ39040828-82C6BB6D-B872-4675-B624-95D5775B2839Q39040855-5B2E56D9-3590-491A-B960-F85C66AD861FQ39391951-578AFB25-21D4-4B50-A350-40ABF4D5CC6EQ39514221-E493BA37-B8A9-4C7A-9766-BC81BC6F9298Q39925250-6D4444B2-2F4F-4368-8879-33329AC3B68BQ40884162-9190FE29-5010-4762-B4E2-AA7D6C4DF4F5Q41631897-2EE8D132-57E9-4691-A5CB-CFE1311955C8Q42428572-BC6C96B1-B5E7-4C7D-A437-558F1DAA9CD3Q45131061-EDFED5E7-7C1F-4D0D-B2A1-0F45E1C65F6FQ47239342-65DAFB35-E118-4251-BCDE-65CCD347BC4AQ47347205-F2225065-C389-478C-BDFB-521567C55679Q47815265-BCFF34AF-A428-4451-922E-F84803528547Q47908597-5FB53850-748C-4728-B9C3-E49512500BCCQ49857850-A08F4D38-E214-4819-A80C-E1C5644009AAQ51577302-9AB95D9F-0970-4A4F-AFC2-C8FC83B3B103Q51632858-A206E728-9DEB-47C4-9039-67741B7AD11CQ55288445-36FA2CB9-075C-4BA4-974C-549B8C31C944
P2860
Epithelial stress and apoptosis underlie Hermansky-Pudlak syndrome-associated interstitial pneumonia
description
2010 nî lūn-bûn
@nan
2010 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@ast
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@en
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@nl
type
label
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@ast
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@en
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@nl
prefLabel
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@ast
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@en
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@nl
P2093
P2860
P50
P1476
Epithelial stress and apoptosi ...... ociated interstitial pneumonia
@en
P2093
Andreas Guenther
Bernadette R Gochuico
Clemens Ruppert
Ingrid Henneke
Martina Korfei
Philipp Markart
Poornima Mahavadi
Saverio Bellusci
P2860
P304
P356
10.1164/RCCM.200909-1414OC
P407
P577
2010-04-08T00:00:00Z