about
Cystic Fibrosis: Lessons from the Sweat GlandThe relevance of sweat testing for the diagnosis of cystic fibrosis in the genomic era.Transepithelial potential difference in cystic fibrosisRescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770The antioxidant role of thiocyanate in the pathogenesis of cystic fibrosis and other inflammation-related diseasesThe ABC protein turned chloride channel whose failure causes cystic fibrosisGuidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus reportPhysiology and pathophysiology of bicarbonate secretion by pancreatic duct epitheliumThe Evolution of Cystic Fibrosis CareCystic fibrosis transmembrane conductance regulator modulators in cystic fibrosis: current perspectivesRetinal stimulates ATP hydrolysis by purified and reconstituted ABCR, the photoreceptor-specific ATP-binding cassette transporter responsible for Stargardt diseaseRole of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosisPathophysiology of gene-targeted mouse models for cystic fibrosisConvulsion and coma after intranasal desmopressin in cystic fibrosisA cluster of negative charges at the amino terminal tail of CFTR regulates ATP-dependent channel gatingPotentiation of ΔF508- and G551D-CFTR-Mediated Cl- Current by Novel HydroxypyrazolinesMicrobial, host and xenobiotic diversity in the cystic fibrosis sputum metabolomeInhibition of CFTR Cl- channel function caused by enzymatic hydrolysis of sphingomyelin.Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation.Chloride uptake into cultured airway epithelial cells from cystic fibrosis patients and normal individuals.Bicarbonate and functional CFTR channel are required for proper mucin secretion and link cystic fibrosis with its mucus phenotype.Bioelectric properties of cystic fibrosis airways obtained at heart-lung transplantation.Genetic markers on chromosome 7.Non-specific activation of the epithelial sodium channel by the CFTR chloride channelComplement yourself: Transcomplementation rescues partially folded mutant proteins.Chloride channels: often enigmatic, rarely predictable.Yet another role for the cystic fibrosis transmembrane conductance regulator.Targets for cystic fibrosis therapy: proteomic analysis and correction of mutant cystic fibrosis transmembrane conductance regulatorMonoclonal antibodies to the apical chloride channel in Necturus gallbladder inhibit the chloride conductanceCl- permeability of human sweat duct cells monitored with fluorescence-digital imaging microscopy: evidence for reduced plasma membrane Cl- permeability in cystic fibrosis.CFTR chloride channel in the apical compartments: spatiotemporal coupling to its interacting partners.VX-809 corrects folding defects in cystic fibrosis transmembrane conductance regulator protein through action on membrane-spanning domain 1.The dual phosphodiesterase 3 and 4 inhibitor RPL554 stimulates CFTR and ciliary beating in primary cultures of bronchial epithelia.Abnormal apical cell membrane in cystic fibrosis respiratory epithelium. An in vitro electrophysiologic analysis.Altered binding of 125I-labeled calmodulin to a 46.5-kilodalton protein in skin fibroblasts cultured from patients with cystic fibrosis.Altered chloride metabolism in cultured cystic fibrosis skin fibroblastsThe cystic fibrosis transmembrane conductance regulator gene.Novel amino-carbonitrile-pyrazole identified in a small molecule screen activates wild-type and ΔF508 cystic fibrosis transmembrane conductance regulator in the absence of a cAMP agonistPulsed direct and constant direct currents in the pilocarpine iontophoresis sweat chloride test.Biogeochemical forces shape the composition and physiology of polymicrobial communities in the cystic fibrosis lung.
P2860
Q22306467-8CC6F10A-94F1-4ECD-99C2-22467B5D0CC2Q24535769-1387CA3B-34EA-497E-AA47-9D2A3D892840Q24563342-73AFE216-2B25-432B-B686-F84311274E64Q24644303-A5412721-E5E8-42CF-9DC9-F16D2AA9D02EQ24655891-EFA60C00-7BE0-4FA7-ACD2-B1B2F7F4B467Q24657572-95445FF8-A116-4222-AD96-F52D12F8EE93Q24657948-E40FF38F-74C8-420F-8779-6ACDAFB4EB27Q26852700-E39D2645-153D-4FA4-A8D0-79264A1FE9DDQ26999299-865BEAFF-C875-47AF-AA38-18D6235E2545Q28073063-046F997F-4C6B-4BB5-BF23-98E5DFC89D60Q28138732-07C82E66-BD9F-4D4D-99B5-2F6B3C2A56C7Q28295024-7B4FDB7B-7081-454D-8E0D-D99B96DD0D0BQ28295602-46CE96A8-0D56-4EAF-B0DC-98328DC380CAQ28361098-831FA66B-7DBD-42E3-973C-F80DB89CD9C0Q28361675-1FC79114-9115-4930-B326-D99D09E30024Q28550065-30F42387-C01F-4F1D-A68E-4458337AB18DQ28829667-84237644-04CD-410F-B99B-1431785BAB11Q30444368-3A4AEA80-C74C-4779-9D5F-B854F93727E1Q30449378-EE4F61B5-0015-4DE2-9E28-60E46D58D761Q30449692-7266B2DA-5DF8-495B-BE99-E8E5F8E2E131Q30522343-1E43CE7F-5EA0-4141-93D4-19D77507434BQ33604580-AC8DD43A-88E0-4298-A0DC-0C22BB35C411Q33676661-EF8F278F-99CC-47DC-BC17-406C20F3130AQ33757239-99C0B7E7-39B2-49BF-BC3B-005E36DEFD95Q33763709-CA56B6A4-087A-4D77-A240-78D457F59F08Q33775731-3A0434BB-BD49-4C3F-ACE0-13D2962FE714Q33806101-EDBA3EA4-1F3F-4758-826D-7BD6D7EDD479Q34082569-1BFAA1E8-3119-4C13-9006-FE73DD68D875Q34309464-249E1B8C-EEF4-4B94-99C5-22C87835ACA1Q34327328-AA7E2B5A-9CD7-4EE8-B322-0BC5575DAC59Q34340439-BAA4D0DA-8097-40E4-BD03-9C7EB955A730Q34362524-22F407FA-ECFF-4E50-9AF9-66451A7C2239Q34500909-E055F6D4-A714-4A1F-B152-CCF56753F100Q34554160-6116CE3B-30DD-4041-B45B-A38B0B04BE8EQ34561780-A8252557-F2CA-413D-B32F-24B862A2701EQ34620126-3511CDC9-9F6E-4837-B590-5CEFD7A7FA08Q34719664-0240ABBB-EC9F-44FB-96E7-1280C0AC9D5DQ34780067-68D2065F-47CB-4639-B377-2568EEF0CE5BQ34915476-52338A38-D1E1-4CD3-869E-9241A0EE6F29Q35124468-7853B4DD-93E2-4B92-B29E-855244ACBB23
P2860
description
1983 nî lūn-bûn
@nan
1983 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
1983 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
1983年の論文
@ja
1983年論文
@yue
1983年論文
@zh-hant
1983年論文
@zh-hk
1983年論文
@zh-mo
1983年論文
@zh-tw
1983年论文
@wuu
name
Chloride impermeability in cystic fibrosis.
@ast
Chloride impermeability in cystic fibrosis.
@en
Chloride impermeability in cystic fibrosis.
@nl
type
label
Chloride impermeability in cystic fibrosis.
@ast
Chloride impermeability in cystic fibrosis.
@en
Chloride impermeability in cystic fibrosis.
@nl
prefLabel
Chloride impermeability in cystic fibrosis.
@ast
Chloride impermeability in cystic fibrosis.
@en
Chloride impermeability in cystic fibrosis.
@nl
P356
P1433
P1476
Chloride impermeability in cystic fibrosis.
@en
P2093
Quinton PM
P2888
P304
P356
10.1038/301421A0
P407
P577
1983-02-01T00:00:00Z
P6179
1012666516