Idebenone increases mitochondrial complex I activity in fibroblasts from LHON patients while producing contradictory effects on respiration.

Idebenone increases mitochondrial complex I activity in fibroblasts from LHON patients while producing contradictory effects on respiration.

Item
http://www.wikidata.org/entity/Q34108909
Mitochondrial disorders: challenges in diagnosis & treatmentProfiling the mitochondrial proteome of Leber's Hereditary Optic Neuropathy (LHON) in Thailand: down-regulation of bioenergetics and mitochondrial protein quality control pathways in fibroblasts with the 11778G>A mutationThe optic nerve: a "mito-window" on mitochondrial neurodegenerationEfficacy and Safety of rAAV2-ND4 Treatment for Leber's Hereditary Optic NeuropathyStem Cell Ophthalmology Treatment Study (SCOTS): bone marrow-derived stem cells in the treatment of Leber's hereditary optic neuropathy.Treatment of hereditary optic neuropathies.Idebenone: A Review in Leber's Hereditary Optic Neuropathy.Leber Hereditary Optic Neuropathy: Exemplar of an mtDNA Disease.The metabolomic signature of Leber's hereditary optic neuropathy reveals endoplasmic reticulum stress.Cyclosporine A does not prevent second-eye involvement in Leber's hereditary optic neuropathy.NMR metabolomics of fibroblasts with inherited mitochondrial Complex I mutation reveals treatment-reversible lipid and amino acid metabolism alterations.
P2860

Idebenone increases mitochondrial complex I activity in fibroblasts from LHON patients while producing contradictory effects on respiration.

Item
http://www.wikidata.org/entity/Q34108909
description
2011 nî lūn-bûn
@nan
2011 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Idebenone increases mitochondr ...... ictory effects on respiration.
@ast
Idebenone increases mitochondr ...... ictory effects on respiration.
@en
Idebenone increases mitochondr ...... ictory effects on respiration.
@nl
type
label
Idebenone increases mitochondr ...... ictory effects on respiration.
@ast
Idebenone increases mitochondr ...... ictory effects on respiration.
@en
Idebenone increases mitochondr ...... ictory effects on respiration.
@nl
prefLabel
Idebenone increases mitochondr ...... ictory effects on respiration.
@ast
Idebenone increases mitochondr ...... ictory effects on respiration.
@en
Idebenone increases mitochondr ...... ictory effects on respiration.
@nl
P1433
P1476
P2093
P2860
P2888
P304
P31
P356
P478
P50
P577
P5875
P6179
P698
P932
P356
P1433
P1476
Idebenone increases mitochondr ...... dictory effects on respiration
@en
P2093
P2860
P2888
P304
P31
P356
P478
P50
P577
P5875
P6179
P698
P932