Inefficiency in GM2 ganglioside elimination by human lysosomal beta-hexosaminidase beta-subunit gene transfer to fibroblastic cell line derived from Sandhoff disease model mice.
about
Therapeutic potential of intracerebroventricular replacement of modified human β-hexosaminidase B for GM2 gangliosidosisTherapeutic response in feline sandhoff disease despite immunity to intracranial gene therapy.Introduction of an N-glycan sequon into HEXA enhances human beta-hexosaminidase cellular uptake in a model of Sandhoff disease.Direct Intracranial Injection of AAVrh8 Encoding Monkey β-N-Acetylhexosaminidase Causes Neurotoxicity in the Primate Brain.
P2860
Inefficiency in GM2 ganglioside elimination by human lysosomal beta-hexosaminidase beta-subunit gene transfer to fibroblastic cell line derived from Sandhoff disease model mice.
description
2006 nî lūn-bûn
@nan
2006 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@ast
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@en
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@nl
type
label
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@ast
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@en
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@nl
prefLabel
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@ast
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@en
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@nl
P2093
P356
P1476
Inefficiency in GM2 gangliosid ...... m Sandhoff disease model mice.
@en
P2093
Aya Kuroki
Daisuke Tsuji
Eri Kawashita
Hitoshi Sakuraba
Kohji Itoh
Shoji Yamanaka
Tomohiro Itakura
Yasuhiro Ishibashi
Yukari Higashine
P304
P356
10.1248/BPB.29.1564
P577
2006-08-01T00:00:00Z