Perturbed interactions of mutant proteolipid protein/DM20 with cholesterol and lipid rafts in oligodendroglia: implications for dysmyelination in spastic paraplegia.
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ERdj4 and ERdj5 are required for endoplasmic reticulum-associated protein degradation of misfolded surfactant protein COligodendroglial membrane dynamics in relation to myelin biogenesisExploring myelin dysfunction in multiple system atrophyThe delicate balance between secreted protein folding and endoplasmic reticulum-associated degradation in human physiologyActin-independent behavior and membrane deformation exhibited by the four-transmembrane protein M6aMAL Is a Regulator of the Recruitment of Myelin Protein PLP to Membrane MicrodomainsNeuronal glycoprotein M6a induces filopodia formation via association with cholesterol-rich lipid raftsA single gene defect causing claustrophobiaDifferent proteolipid protein mutants exhibit unique metabolic defects.Lipid metabolism in myelinating glial cells: lessons from human inherited disorders and mouse models.Neurotransmitter-triggered transfer of exosomes mediates oligodendrocyte-neuron communication.Targeted metabolomic analyses of cellular models of pelizaeus-merzbacher disease reveal plasmalogen and myo-inositol solute carrier dysfunction.Performance of protein disorder prediction programs on amino acid substitutions.Structure-function analysis of human stomatin: A mutation studyCholesterol Biosynthesis Supports Myelin Gene Expression and Axon Ensheathment through Modulation of P13K/Akt/mTor Signaling.The molecular and cellular defects underlying Pelizaeus-Merzbacher disease.Myelin proteomics: molecular anatomy of an insulating sheath.Differences in endoplasmic-reticulum quality control determine the cellular response to disease-associated mutants of proteolipid protein.Expression of proteolipid protein gene in spinal cord stem cells and early oligodendrocyte progenitor cells is dispensable for normal cell migration and myelination.On the biogenesis of myelin membranes: sorting, trafficking and cell polarity.Progesterone antagonist therapy in a Pelizaeus-Merzbacher mouse model.Regulation and roles of neuronal diacylglycerol kinases: a lipid perspective.Axon-glia interaction and membrane traffic in myelin formation.Activation of oligodendroglial Fyn kinase enhances translation of mRNAs transported in hnRNP A2-dependent RNA granules.Extracellular vesicle sorting of α-Synuclein is regulated by sumoylation.Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.Cell-specific loss of kappa-opioid receptors in oligodendrocytes of the dysmyelinating jimpy mouse.Heterogeneous nuclear ribonucleoprotein (hnRNP) F is a novel component of oligodendroglial RNA transport granules contributing to regulation of myelin basic protein (MBP) synthesis.Filopodia formation driven by membrane glycoprotein M6a depends on the interaction of its transmembrane domains.Transcriptional expression of myelin basic protein in oligodendrocytes depends on functional syntaxin 4: a potential correlation with autocrine signaling.Attenuation of endoplasmic reticulum stress in Pelizaeus-Merzbacher disease by an anti-malaria drug, chloroquine.The Membrane Glycoprotein M6a Endocytic/Recycling Pathway Involves Clathrin-Mediated Endocytosis and Affects Neuronal SynapsesThe major myelin-resident protein PLP is transported to myelin membranes via a transcytotic mechanism: involvement of sulfatide.Cholesterol interaction with the related steroidogenic acute regulatory lipid-transfer (START) domains of StAR (STARD1) and MLN64 (STARD3).LRP1 regulates peroxisome biogenesis and cholesterol homeostasis in oligodendrocytes and is required for proper CNS myelin development and repair.The wmN1 enhancer region in intron 1 is required for expression of human PLP1.Chemical Screening Identifies Enhancers of Mutant Oligodendrocyte Survival and Unmasks a Distinct Pathological Phase in Pelizaeus-Merzbacher Disease
P2860
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P2860
Perturbed interactions of mutant proteolipid protein/DM20 with cholesterol and lipid rafts in oligodendroglia: implications for dysmyelination in spastic paraplegia.
description
2006 nî lūn-bûn
@nan
2006 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
Perturbed interactions of muta ...... ination in spastic paraplegia.
@ast
Perturbed interactions of muta ...... ination in spastic paraplegia.
@en
Perturbed interactions of muta ...... ination in spastic paraplegia.
@nl
type
label
Perturbed interactions of muta ...... ination in spastic paraplegia.
@ast
Perturbed interactions of muta ...... ination in spastic paraplegia.
@en
Perturbed interactions of muta ...... ination in spastic paraplegia.
@nl
prefLabel
Perturbed interactions of muta ...... ination in spastic paraplegia.
@ast
Perturbed interactions of muta ...... ination in spastic paraplegia.
@en
Perturbed interactions of muta ...... ination in spastic paraplegia.
@nl
P2093
P1476
Perturbed interactions of muta ...... lination in spastic paraplegia
@en
P2093
Christoph Thiele
Jacqueline Trotter
Katja Gehrig-Burger
Klaus-Armin Nave
P304
11743-11752
P356
10.1523/JNEUROSCI.3581-06.2006
P407
P577
2006-11-01T00:00:00Z