Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia. - Wikidata - wikimedia - TriplyDB

Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia.

Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia.

http://www.wikidata.org/entity/Q34671320

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Transgenic hCFTR expression fails to correct β-ENaC mouse lung disease Epithelial Anion Transport as Modulator of Chemokine Signaling Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences Molecular mechanism of pancreatic and salivary gland fluid and HCO3 secretion Midkine in host defence Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats Method for quantitative study of airway functional microanatomy using micro-optical coherence tomography Understanding protein kinase CK2 mis-regulation upon F508del CFTR expression pH Dependent Antimicrobial Peptides and Proteins, Their Mechanisms of Action and Potential as Therapeutic Agents CFTR Modulators: Shedding Light on Precision Medicine for Cystic Fibrosis Origins of cystic fibrosis lung disease Airway Gland Structure and Function Defective CFTR expression and function are detectable in blood monocytes: development of a new blood test for cystic fibrosis Bicarbonate and functional CFTR channel are required for proper mucin secretion and link cystic fibrosis with its mucus phenotype.Assessing mucociliary transport of single particles in vivo shows variable speed and preference for the ventral trachea in newborn pigs Marked increases in mucociliary clearance produced by synergistic secretory agonists or inhibition of the epithelial sodium channel.Neonates with cystic fibrosis have a reduced nasal liquid pH; a small pilot study.Lung phenotype of juvenile and adult cystic fibrosis transmembrane conductance regulator-knockout ferrets.Porcine nasal epithelial cultures for studies of cystic fibrosis sinusitis Physiology of epithelial chloride and fluid secretion A functional anatomic defect of the cystic fibrosis airway.Physiological levels of lipoxin A4 inhibit ENaC and restore airway surface liquid height in cystic fibrosis bronchial epithelium CFTR and lung homeostasis.pH modulates the activity and synergism of the airway surface liquid antimicrobials β-defensin-3 and LL-37 The ΔF508 mutation causes CFTR misprocessing and cystic fibrosis-like disease in pigs.Human cystic fibrosis airway epithelia have reduced Cl- conductance but not increased Na+ conductance.Animal models of gastrointestinal and liver diseases. Animal models of cystic fibrosis: gastrointestinal, pancreatic, and hepatobiliary disease and pathophysiology.Hybrid nonviral/viral vector systems for improved piggyBac DNA transposon in vivo delivery Hypoxia down-regulates expression of secretory leukocyte protease inhibitor in bronchial epithelial cells via TGF-β1 Cystic Fibrosis Gene Therapy in the UK and Elsewhere.Endogenous surface expression of ΔF508-CFTR mediates cAMP-stimulated Cl(-) current in CFTR(ΔF508/ΔF508) pig thyroid epithelial cells Recent advances in understanding and managing cystic fibrosis transmembrane conductance regulator dysfunction.Mutating the Conserved Q-loop Glutamine 1291 Selectively Disrupts Adenylate Kinase-dependent Channel Gating of the ATP-binding Cassette (ABC) Adenylate Kinase Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) and Reduces Channel Function in Genetic and epigenetic inactivation of extracellular superoxide dismutase promotes an invasive phenotype in human lung cancer by disrupting ECM homeostasis.Defective innate immunity and hyperinflammation in newborn cystic fibrosis transmembrane conductance regulator-knockout ferret lungs A role for two-pore K⁺ channels in modulating Na⁺ absorption and Cl⁻ secretion in normal human bronchial epithelial cells A spatial model of fluid recycling in the airways of the lung.Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung.CFTR is required for maximal transepithelial liquid transport in pig alveolar epithelia.Transcriptional targeting in the airway using novel gene regulatory elements.

P2860

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P2860

Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia.

http://www.wikidata.org/entity/Q34671320

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2010 nî lūn-bûn

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2010 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած

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Alejandro A Pezzulo

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David A Stoltz

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Janice L Launspach

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Jeng-Haur Chen

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Joseph Zabner

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Kathryn Chaloner

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Leah R Reznikov

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Michael V Rector

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Philip H Karp

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P2860

Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

Cystic Fibrosis: Lessons from the Sweat Gland

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

Lung symptoms in pseudohypoaldosteronism type 1 are associated with deficiency of the alpha-subunit of the epithelial sodium channel

Cystic fibrosis

Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice

Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer

Structure and function of the CFTR chloride channel

Pathophysiology of gene-targeted mouse models for cystic fibrosis

Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation.

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