Human cystic fibrosis airway epithelia have reduced Cl- conductance but not increased Na+ conductance.
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Nedd4-2 and the regulation of epithelial sodium transportTransgenic hCFTR expression fails to correct β-ENaC mouse lung diseaseEpithelial Anion Transport as Modulator of Chemokine SignalingCharacterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout ratsCFTR Modulators: Shedding Light on Precision Medicine for Cystic FibrosisOrigins of cystic fibrosis lung diseaseAirway Gland Structure and FunctionActivation of the epithelial sodium channel (ENaC) by the alkaline protease from Pseudomonas aeruginosaStarting a lung transplant program: a roadmap for long-term excellenceMarked increases in mucociliary clearance produced by synergistic secretory agonists or inhibition of the epithelial sodium channel.Lung structure and function similarities between primary ciliary dyskinesia and mild cystic fibrosis: a pilot studyInter-α-inhibitor blocks epithelial sodium channel activation and decreases nasal potential differences in ΔF508 mice.A functional anatomic defect of the cystic fibrosis airway.CFTR and lung homeostasis.ENaCs and ASICs as therapeutic targets.Sinus hypoplasia precedes sinus infection in a porcine model of cystic fibrosis.Regulation of transport in the connecting tubule and cortical collecting ductThe innate immune function of airway epithelial cells in inflammatory lung diseaseStatus of fluid and electrolyte absorption in cystic fibrosis.Inhibition of airway surface fluid absorption by cholinergic stimulationLiquid hyper-absorption as a cause of increased DTPA clearance in the cystic fibrosis airwayElectrolyte transport properties in distal small airways from cystic fibrosis pigs with implications for host defense.Relationships among CFTR expression, HCO3- secretion, and host defense may inform gene- and cell-based cystic fibrosis therapiesNonantibiotic macrolides prevent human neutrophil elastase-induced mucus stasis and airway surface liquid volume depletion.Lessons learned from the cystic fibrosis pig.Reduced sodium transport with nasal administration of the prostasin inhibitor camostat in subjects with cystic fibrosis.Role of CFTR in epithelial physiology.Ion transport by pulmonary epithelia.Lactoferrin: an alternative view of its role in human biological fluids.Proteases, cystic fibrosis and the epithelial sodium channel (ENaC).Failure of respiratory defenses in the pathogenesis of bacterial pneumonia of cattle.Tailored Pig Models for Preclinical Efficacy and Safety Testing of Targeted Therapies.CFTR and Ca Signaling in Cystic Fibrosis.NVP-QBE170: an inhaled blocker of the epithelial sodium channel with a reduced potential to induce hyperkalaemia.Correction of CFTR function in nasal epithelial cells from cystic fibrosis patients predicts improvement of respiratory function by CFTR modulators.Efficient delivery of RNA interference oligonucleotides to polarized airway epithelia in vitroThe CFTR and ENaC debate: how important is ENaC in CF lung disease?The role of CFTR in transepithelial liquid transport in pig alveolar epithelia.Increased apical Na+ permeability in cystic fibrosis is supported by a quantitative model of epithelial ion transport.Epithelial sodium channel silencing as a strategy to correct the airway surface fluid deficit in cystic fibrosis.
P2860
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P2860
Human cystic fibrosis airway epithelia have reduced Cl- conductance but not increased Na+ conductance.
description
2011 nî lūn-bûn
@nan
2011 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի հունիսին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Human cystic fibrosis airway e ...... not increased Na+ conductance.
@ast
Human cystic fibrosis airway e ...... not increased Na+ conductance.
@en
type
label
Human cystic fibrosis airway e ...... not increased Na+ conductance.
@ast
Human cystic fibrosis airway e ...... not increased Na+ conductance.
@en
prefLabel
Human cystic fibrosis airway e ...... not increased Na+ conductance.
@ast
Human cystic fibrosis airway e ...... not increased Na+ conductance.
@en
P2093
P2860
P356
P1476
Human cystic fibrosis airway e ...... not increased Na+ conductance
@en
P2093
Jeng-Haur Chen
Kalpaj Parekh
Michael J Welsh
Omar A Itani
Philip H Karp
Sarah Ernst
Shaf Keshavjee
P2860
P304
10260-10265
P356
10.1073/PNAS.1106695108
P407
P577
2011-06-06T00:00:00Z