Fine structural observations of neurofilamentous changes in amyotrophic lateral sclerosis.
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Ultrastructural studies of ALS mitochondria connect altered function and permeability with defects of mitophagy and mitochondriogenesisRedox regulation in amyotrophic lateral sclerosisUltrastructural study of Betz cells in the primary motor cortex of the human brainPeptidyl-prolyl isomerase 1 regulates protein phosphatase 2A-mediated topographic phosphorylation of neurofilament proteinsTargeted disruption of the cyclin-dependent kinase 5 gene results in abnormal corticogenesis, neuronal pathology and perinatal deathProtein Homeostasis in Amyotrophic Lateral Sclerosis: Therapeutic Opportunities?Animal models of Kennedy disease.Abnormalities of Mitochondrial Dynamics in Neurodegenerative Diseases.Altered axonal architecture by removal of the heavily phosphorylated neurofilament tail domains strongly slows superoxide dismutase 1 mutant-mediated ALS.A simple test to monitor the motor dysfunction in a transgenic mouse model of amyotrophic lateral sclerosisMisfolded SOD1 associated with motor neuron mitochondria alters mitochondrial shape and distribution prior to clinical onset.Variations in the progranulin gene affect global gene expression in frontotemporal lobar degenerationMitochondrial dysfunction and intracellular calcium dysregulation in ALSMisfolded mutant SOD1 directly inhibits VDAC1 conductance in a mouse model of inherited ALSALS-linked mutant superoxide dismutase 1 (SOD1) alters mitochondrial protein composition and decreases protein import.Genetic rodent models of amyotrophic lateral sclerosisPhosphatidylinositol phosphates directly bind to neurofilament light chain (NF-L) for the regulation of NF-L self assemblyThe structural biochemistry of the superoxide dismutases.Gamma-synuclein pathology in amyotrophic lateral sclerosisMuscle pathology without severe nerve pathology in a new mouse model of Charcot-Marie-Tooth disease type 2E.Mitochondria-targeted catalase reverts the neurotoxicity of hSOD1G⁹³A astrocytes without extending the survival of ALS-linked mutant hSOD1 miceA fruitful endeavor: modeling ALS in the fruit flyMitochondrial medicine for aging and neurodegenerative diseasesQuantitative ultrastructural analysis of a single spinal cord demyelinated lesion predicts total lesion load, axonal loss, and neurological dysfunction in a murine model of multiple sclerosisA Stochastic Multiscale Model That Explains the Segregation of Axonal Microtubules and Neurofilaments in Neurological Diseases.Mitochondria as a therapeutic target for aging and neurodegenerative diseases.Mitochondrial dynamic abnormalities in amyotrophic lateral sclerosis.Neurofilament Phosphorylation during Development and Disease: Which Came First, the Phosphorylation or the Accumulation?Proximal giant neurofilamentous axonopathy in mice genetically engineered to resist calpain and caspase cleavage of α-II spectrin.Dysregulated expression of death, stress and mitochondrion related genes in the sciatic nerve of presymptomatic SOD1(G93A) mouse model of Amyotrophic Lateral Sclerosis.RNAseq Analyses Identify Tumor Necrosis Factor-Mediated Inflammation as a Major Abnormality in ALS Spinal Cord.Peripherin is a subunit of peripheral nerve neurofilaments: implications for differential vulnerability of CNS and peripheral nervous system axons.Increasing neurofilament subunit NF-M expression reduces axonal NF-H, inhibits radial growth, and results in neurofilamentous accumulation in motor neurons.Neurofilament subunit NF-H modulates axonal diameter by selectively slowing neurofilament transportCompartment-dependent mitochondrial alterations in experimental ALS, the effects of mitophagy and mitochondriogenesisRapid movements of vimentin on microtubule tracks: kinesin-dependent assembly of intermediate filament networksSlow axonal transport of neurofilament protein in cultured neurons.Absence of neurofilaments reduces the selective vulnerability of motor neurons and slows disease caused by a familial amyotrophic lateral sclerosis-linked superoxide dismutase 1 mutantSynaptic sprouting increases the uptake capacities of motoneurons in amyotrophic lateral sclerosis miceSelective association of misfolded ALS-linked mutant SOD1 with the cytoplasmic face of mitochondria.
P2860
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P2860
Fine structural observations of neurofilamentous changes in amyotrophic lateral sclerosis.
description
1984 nî lūn-bûn
@nan
1984 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
1984 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
1984年の論文
@ja
1984年論文
@yue
1984年論文
@zh-hant
1984年論文
@zh-hk
1984年論文
@zh-mo
1984年論文
@zh-tw
1984年论文
@wuu
name
Fine structural observations o ...... amyotrophic lateral sclerosis.
@ast
Fine structural observations o ...... amyotrophic lateral sclerosis.
@en
Fine structural observations o ...... amyotrophic lateral sclerosis.
@nl
type
label
Fine structural observations o ...... amyotrophic lateral sclerosis.
@ast
Fine structural observations o ...... amyotrophic lateral sclerosis.
@en
Fine structural observations o ...... amyotrophic lateral sclerosis.
@nl
prefLabel
Fine structural observations o ...... amyotrophic lateral sclerosis.
@ast
Fine structural observations o ...... amyotrophic lateral sclerosis.
@en
Fine structural observations o ...... amyotrophic lateral sclerosis.
@nl
P2093
P1476
Fine structural observations o ...... amyotrophic lateral sclerosis.
@en
P2093
P304
P577
1984-09-01T00:00:00Z