Defects in mitochondrial ATP synthesis in dystrophin-deficient mdx skeletal muscles may be caused by complex I insufficiency.
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Metabogenic and Nutriceutical Approaches to Address Energy Dysregulation and Skeletal Muscle Wasting in Duchenne Muscular DystrophyAttempting to Compensate for Reduced Neuronal Nitric Oxide Synthase Protein with Nitrate Supplementation Cannot Overcome Metabolic Dysfunction but Rather Has Detrimental Effects in Dystrophin-Deficient mdx Muscle.Muscle Transcriptional Profile Based on Muscle Fiber, Mitochondrial Respiratory Activity, and Metabolic Enzymes.Hypoxia-induced cardiac injury in dystrophic mice.Enhanced Energetic State and Protection from Oxidative Stress in Human Myoblasts Overexpressing BMI1.Mass spectrometry-based protein analysis to unravel the tissue pathophysiology in Duchenne muscular dystrophy.Progressive muscle proteome changes in a clinically relevant pig model of Duchenne muscular dystrophy.Therapeutic strategies to address neuronal nitric oxide synthase deficiency and the loss of nitric oxide bioavailability in Duchenne Muscular Dystrophy.Muscle biopsies from human muscle diseases with myopathic pathology reveal common alterations in mitochondrial function.Loss of NAD Homeostasis Leads to Progressive and Reversible Degeneration of Skeletal MuscleLoss of MKP-5 promotes myofiber survival by activating STAT3/Bcl-2 signaling during regenerative myogenesis.Pharmacological inhibition of REV-ERB stimulates differentiation, inhibits turnover and reduces fibrosis in dystrophic muscle.Comparative gel-based proteomic analysis of chemically crosslinked complexes in dystrophic skeletal muscle.Expression profiling of disease progression in canine model of Duchenne muscular dystrophy.Skeletal Muscle Metabolism in Duchenne and Becker Muscular Dystrophy-Implications for Therapies.
P2860
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P2860
Defects in mitochondrial ATP synthesis in dystrophin-deficient mdx skeletal muscles may be caused by complex I insufficiency.
description
2014 nî lūn-bûn
@nan
2014 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2014 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2014年の論文
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2014年学术文章
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2014年学术文章
@zh-cn
2014年学术文章
@zh-hans
2014年学术文章
@zh-my
2014年学术文章
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2014年學術文章
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name
Defects in mitochondrial ATP s ...... ed by complex I insufficiency.
@ast
Defects in mitochondrial ATP s ...... ed by complex I insufficiency.
@en
Defects in mitochondrial ATP s ...... ed by complex I insufficiency.
@nl
type
label
Defects in mitochondrial ATP s ...... ed by complex I insufficiency.
@ast
Defects in mitochondrial ATP s ...... ed by complex I insufficiency.
@en
Defects in mitochondrial ATP s ...... ed by complex I insufficiency.
@nl
prefLabel
Defects in mitochondrial ATP s ...... ed by complex I insufficiency.
@ast
Defects in mitochondrial ATP s ...... ed by complex I insufficiency.
@en
Defects in mitochondrial ATP s ...... ed by complex I insufficiency.
@nl
P2093
P2860
P50
P1433
P1476
Defects in mitochondrial ATP s ...... sed by complex I insufficiency
@en
P2093
Alan Hayes
Andrew D Williams
Cara A Timpani
Emma Rybalka
Matthew B Cooke
P2860
P304
P356
10.1371/JOURNAL.PONE.0115763
P407
P577
2014-12-26T00:00:00Z