Early axonal loss accompanied by impaired endocytosis, abnormal axonal transport, and decreased microtubule stability occur in the model of Krabbe's disease.
about
Myelin damage and repair in pathologic CNS: challenges and prospectsLysosomal Re-acidification Prevents Lysosphingolipid-Induced Lysosomal Impairment and Cellular ToxicityCombined gene/cell therapies provide long-term and pervasive rescue of multiple pathological symptoms in a murine model of globoid cell leukodystrophy.Mechanism of neuromuscular dysfunction in Krabbe disease.How membrane dysfunction influences neuronal survival pathways in sphingolipid storage disordersPatient fibroblasts-derived induced neurons demonstrate autonomous neuronal defects in adult-onset Krabbe disease.Synaptic failure: The achilles tendon of sphingolipidosesLysosomal enzyme replacement therapies: Historical development, clinical outcomes, and future perspectives.Inherited and acquired disorders of myelin: The underlying myelin pathology.Ultrastructural Characterization of the Lower Motor System in a Mouse Model of Krabbe Disease.Role of extracellular calcium and mitochondrial oxygen species in psychosine-induced oligodendrocyte cell death.Lysosphingolipids and sphingolipidoses: Psychosine in Krabbe's disease.Axonal pathology in Krabbe's disease: The cytoskeleton as an emerging therapeutic target.Treatment for Krabbe's disease: Finding the combination.Perspective on innovative therapies for globoid cell leukodystrophy.A Comparative Study on the Alterations of Endocytic Pathways in Multiple Lysosomal Storage Disorders.Midbrain morphology reflects extent of brain damage in Krabbe disease.Long-Term Improvement of Neurological Signs and Metabolic Dysfunction in a Mouse Model of Krabbe's Disease after Global Gene Therapy.Human iPSC-based models highlight defective glial and neuronal differentiation from neural progenitor cells in metachromatic leukodystrophy.Is Parkinson's disease a lysosomal disorder?
P2860
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P2860
Early axonal loss accompanied by impaired endocytosis, abnormal axonal transport, and decreased microtubule stability occur in the model of Krabbe's disease.
description
2014 nî lūn-bûn
@nan
2014 թուականի Մարտին հրատարակուած գիտական յօդուած
@hyw
2014 թվականի մարտին հրատարակված գիտական հոդված
@hy
2014年の論文
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2014年論文
@yue
2014年論文
@zh-hant
2014年論文
@zh-hk
2014年論文
@zh-mo
2014年論文
@zh-tw
2014年论文
@wuu
name
Early axonal loss accompanied ...... the model of Krabbe's disease.
@ast
Early axonal loss accompanied ...... the model of Krabbe's disease.
@en
type
label
Early axonal loss accompanied ...... the model of Krabbe's disease.
@ast
Early axonal loss accompanied ...... the model of Krabbe's disease.
@en
prefLabel
Early axonal loss accompanied ...... the model of Krabbe's disease.
@ast
Early axonal loss accompanied ...... the model of Krabbe's disease.
@en
P2093
P2860
P50
P1476
Early axonal loss accompanied ...... the model of Krabbe's disease.
@en
P2093
Ana Rita Malheiro
Melani Solomon
Vera Filipe Sousa
P2860
P304
P356
10.1016/J.NBD.2014.02.012
P50
P577
2014-03-06T00:00:00Z