Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.
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Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and DivergencesLoss of cftr function leads to pancreatic destruction in larval zebrafish.Origins of cystic fibrosis lung diseaseDefective goblet cell exocytosis contributes to murine cystic fibrosis-associated intestinal disease.Tissue and cellular expression patterns of porcine CFTR: similarities to and differences from human CFTRGel-forming mucins form distinct morphologic structures in airwaysCystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth.Defective fluid secretion from submucosal glands of nasal turbinates from CFTR-/- and CFTR (ΔF508/ΔF508) pigs.Parasympathetic innervation regulates tubulogenesis in the developing salivary gland.Pseudomonas aeruginosa triggers CFTR-mediated airway surface liquid secretion in swine trachea.Variation in MSRA modifies risk of neonatal intestinal obstruction in cystic fibrosis.Loss of cystic fibrosis transmembrane conductance regulator function produces abnormalities in tracheal development in neonatal pigs and young children.Cystic fibrosis transmembrane conductance regulator with a shortened R domain rescues the intestinal phenotype of CFTR-/- mice.Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia.Multicenter intestinal current measurements in rectal biopsies from CF and non-CF subjects to monitor CFTR function.The ΔF508 mutation causes CFTR misprocessing and cystic fibrosis-like disease in pigs.Human cystic fibrosis airway epithelia have reduced Cl- conductance but not increased Na+ conductance.Glycaemic regulation and insulin secretion are abnormal in cystic fibrosis pigs despite sparing of islet cell mass.Swine models of cystic fibrosis reveal male reproductive tract phenotype at birth.Animal models of gastrointestinal and liver diseases. Animal models of cystic fibrosis: gastrointestinal, pancreatic, and hepatobiliary disease and pathophysiology.Ferret and pig models of cystic fibrosis: prospects and promise for gene therapy.An activated immune and inflammatory response targets the pancreas of newborn pigs with cystic fibrosisGenetically engineered pig models for human diseases.The obesity epidemic: from the environment to epigenetics - not simply a response to dietary manipulation in a thermoneutral environmentThe porcine chloride channel calcium-activated family member pCLCA4a mirrors lung expression of the human hCLCA4.Excess Secretion of Gel-Forming Mucins and Associated Innate Defense Proteins with Defective Mucin Un-Packaging Underpin Gallbladder Mucocele Formation in Dogs.Naturally Occurring Deletion Mutants of the Pig-Specific, Intestinal Crypt Epithelial Cell Protein CLCA4b without Apparent Phenotype.Computed Tomography (CT) Scanning Facilitates Early Identification of Neonatal Cystic Fibrosis PigletsAdvances in cell and gene-based therapies for cystic fibrosis lung diseasePancreatic damage in fetal and newborn cystic fibrosis pigs involves the activation of inflammatory and remodeling pathwaysGenetically modified species in research: Opportunities and challenges for the histology core laboratory.Acid-Sensing Ion Channel 1a Contributes to Airway Hyperreactivity in Mice.The Enigmatic Gut in Cystic Fibrosis: Linking Inflammation, Dysbiosis, and the Increased Risk of Malignancy.Pancreatic and biliary secretion are both altered in cystic fibrosis pigs.Pancreatic pathophysiology in cystic fibrosis.Cellular chloride and bicarbonate retention alters intracellular pH regulation in Cftr KO crypt epithelium.The cystic fibrosis gene: a molecular genetic perspectiveNew animal models of cystic fibrosis: what are they teaching us?Cystic Fibrosis Transmembrane Conductance Regulator in Sarcoplasmic Reticulum of Airway Smooth Muscle. Implications for Airway ContractilityComparative biology of cystic fibrosis animal models
P2860
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P2860
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.
description
2010 nî lūn-bûn
@nan
2010 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.
@ast
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.
@en
type
label
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.
@ast
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.
@en
prefLabel
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.
@ast
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.
@en
P2093
P2860
P1476
Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.
@en
P2093
Alejandro A Pezzulo
David A Stoltz
David K Meyerholz
Michael J Welsh
P2860
P304
P356
10.2353/AJPATH.2010.090849
P407
P577
2010-01-28T00:00:00Z