Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse. - Wikidata - wikimedia - TriplyDB

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

http://www.wikidata.org/entity/Q35493060

about

Skeletal muscle laminin and MDC1A: pathogenesis and treatment strategies.Form and function: the laminin family of heterotrimers Increasing complexity of the dystrophin-associated protein complex Distinct roles for laminin globular domains in laminin alpha1 chain mediated rescue of murine laminin alpha2 chain deficiency A role of dystroglycan in schwannoma cell adhesion to laminin Dystroglycan is a binding protein of laminin and merosin in peripheral nerve Mild congenital muscular dystrophy in two patients with an internally deleted laminin alpha2-chain Integrins (alpha7beta1) in muscle function and survival. Disrupted expression in merosin-deficient congenital muscular dystrophy The absence of nidogen 1 does not affect murine basement membrane formation High RhoA activity maintains the undifferentiated mesenchymal cell phenotype, whereas RhoA down-regulation by laminin-2 induces smooth muscle myogenesis Distribution and function of laminins in the neuromuscular system of developing, adult, and mutant mice The super super-healing MRL mouse strain Regulation of radial glial survival by signals from the meninges.Amelioration of laminin-alpha2-deficient congenital muscular dystrophy by somatic gene transfer of miniagrin.Laminins of the neuromuscular system.Laminins and human disease.Differential heparin inhibition of skeletal muscle alpha-dystroglycan binding to laminins.Adenovirus mediated gene transfer to skeletal muscle.Elimination of myostatin does not combat muscular dystrophy in dy mice but increases postnatal lethality.The muscular dystrophies: from genes to therapies.Overexpression of the cytotoxic T cell (CT) carbohydrate inhibits muscular dystrophy in the dyW mouse model of congenital muscular dystrophy 1A.Comparative proteomic profiling of dystroglycan-associated proteins in wild type, mdx, and Galgt2 transgenic mouse skeletal muscle.Distribution of alpha-dystroglycan during embryonic nerve-muscle synaptogenesis.Non-muscle alpha-dystroglycan is involved in epithelial development.Partial laminin alpha2 chain restoration in alpha2 chain-deficient dy/dy mouse by primary muscle cell culture transplantation Merosin and laminin in myogenesis; specific requirement for merosin in myotube stability and survival.Differential expression of mRNAs encoding laminin chain variants during in vitro development of mouse blastocysts alpha-Dystroglycan is a laminin receptor involved in extracellular matrix assembly on myotubes and muscle cell viability.Targeted disruption of the LAMA3 gene in mice reveals abnormalities in survival and late stage differentiation of epithelial cells.Animal models for muscular dystrophy show different patterns of sarcolemmal disruption.Membrane targeting and stabilization of sarcospan is mediated by the sarcoglycan subcomplex.Gamma-sarcoglycan deficiency leads to muscle membrane defects and apoptosis independent of dystrophin.A recombinant tail-less integrin beta 4 subunit disrupts hemidesmosomes, but does not suppress alpha 6 beta 4-mediated cell adhesion to laminins.Laminin-211 in skeletal muscle function.Animal models of muscular dystrophy Muscular dystrophy associated with alpha-dystroglycan deficiency in Sphynx and Devon Rex cats.Overexpression of Galgt2 reduces dystrophic pathology in the skeletal muscles of alpha sarcoglycan-deficient mice Merosin-deficient congenital muscular dystrophy. Partial genetic correction in two mouse models Skeletal muscle as a paradigm for regenerative biology and medicine.Congenital muscular dystrophy. Part II: a review of pathogenesis and therapeutic perspectives.

P2860

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P2860

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

http://www.wikidata.org/entity/Q35493060

description

1994 nî lūn-bûn

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1994 թուականի Յունիսին հրատարակուած գիտական յօդուած

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1994 թվականի հունիսին հրատարակված գիտական հոդված

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1994年の論文

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1994年論文

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1994年論文

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1994年論文

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1994年論文

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1994年論文

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1994年论文

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name

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

@ast

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

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type

label

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

@ast

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

@en

prefLabel

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

@ast

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

@en

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Proceedings of the National Academy of Sciences of the United States of America

P1476

Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.

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P2093

Christmas P

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Engvall E

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Wewer UM

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P2860

Molecular heterogeneity of basal laminae: isoforms of laminin and collagen IV at the neuromuscular junction and elsewhere

Distribution and isolation of four laminin variants; tissue restricted distribution of heterotrimers assembled from five different subunits

Merosin, a tissue-specific basement membrane protein, is a laminin-like protein

Tissue distribution of the dystrophin-related gene product and expression in the mdx and dy mouse

Human laminin M chain (merosin): complete primary structure, chromosomal assignment, and expression of the M and A chain in human fetal tissues

Deficiency of the 50K dystrophin-associated glycoprotein in severe childhood autosomal recessive muscular dystrophy

Localisation of a dystrophin-related autosomal gene to 6q24 in man, and to mouse chromosome 10 in the region of the dystrophia muscularis (dy) locus

Localization of a gene for Fukuyama type congenital muscular dystrophy to chromosome 9q31-33

A laminin-like adhesive protein concentrated in the synaptic cleft of the neuromuscular junction

Association of dystrophin-related protein with dystrophin-associated proteins in mdx mouse muscle

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