Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2
about
The molecular pathology of primary immunodeficienciesIdentification of a missense mutation (G329A;Arg(110)--> GLN) in the human FUT7 geneReactive oxygen species in inflammation and tissue injuryProtein glycosylation in development and disease.Genes that regulate eosinophilic inflammation.Mechanisms and consequences of phagocyte adhesion to endothelium.Impairment of the Golgi GDP-L-fucose transport and unresponsiveness to fucose replacement therapy in LAD II patients.Syndromic immunodeficiencies: genetic syndromes associated with immune abnormalities.Infectious susceptibility and severe deficiency of leukocyte rolling and recruitment in E-selectin and P-selectin double mutant miceTherapeutic inhibition of carbohydrate-protein interactions in vivo.Human deficiencies of fucosylation and sialylation affecting selectin ligands.Intracellular signalling during neutrophil recruitment.Differential interactions of heparin and heparan sulfate glycosaminoglycans with the selectins. Implications for the use of unfractionated and low molecular weight heparins as therapeutic agents.Leukocyte Adhesion Deficiency Type II is a generalized defect of de novo GDP-fucose biosynthesis. Endothelial cell fucosylation is not required for neutrophil rolling on human nonlymphoid endothelium.Chemerin15 inhibits neutrophil-mediated vascular inflammation and myocardial ischemia-reperfusion injury through ChemR23.Potential pro-inflammatory effects of soluble E-selectin upon neutrophil function.Core 2 oligosaccharides mediate eosinophil and neutrophil peritoneal but not lung recruitment.Defective intracellular activity of GDP-D-mannose-4,6-dehydratase in leukocyte adhesion deficiency type II syndrome.
P2860
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P2860
Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2
description
1995 nî lūn-bûn
@nan
1995年の論文
@ja
1995年論文
@yue
1995年論文
@zh-hant
1995年論文
@zh-hk
1995年論文
@zh-mo
1995年論文
@zh-tw
1995年论文
@wuu
1995年论文
@zh
1995年论文
@zh-cn
name
Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2
@ast
Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2
@en
type
label
Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2
@ast
Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2
@en
prefLabel
Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2
@ast
Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2
@en
P2093
P2860
P356
P1476
Neutrophil adhesion in leukocyte adhesion deficiency syndrome type 2
@en
P2093
Paulson JC
Phillips ML
Schwartz BR
P2860
P304
P356
10.1172/JCI118361
P407
P577
1995-12-01T00:00:00Z