Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I.
about
Inherited metabolic disease in companion animals: searching for nature's mistakesalpha-Galactosidase A deficient mice: a model of Fabry diseasePentosan Polysulfate: Oral Versus Subcutaneous Injection in Mucopolysaccharidosis Type I DogsReplacing the enzyme alpha-L-iduronidase at birth ameliorates symptoms in the brain and periphery of dogs with mucopolysaccharidosis type I.Decreased performance in IDUA knockout mouse mimic limitations of joint function and locomotion in patients with Hurler syndromeArylsulfatase B-deficient mucopolysaccharidosis in rats.Safe, efficient, and reproducible gene therapy of the brain in the dog models of Sanfilippo and Hurler syndromes.Bone marrow transplantation in canine mucopolysaccharidosis I. Effects within the central nervous system.Cardiac manifestations in the mouse model of mucopolysaccharidosis I.Cardiac disease in mucopolysaccharidosis type I attributed to catecholaminergic and hemodynamic deficiencies.Characterization of an immunodeficient mouse model of mucopolysaccharidosis type I suitable for preclinical testing of human stem cell and gene therapy.Arterial pathology in canine mucopolysaccharidosis-I and response to therapyMagnetic resonance findings of the corpus callosum in canine and feline lysosomal storage diseasesGlycosaminoglycan storage in neuroanatomical regions of mucopolysaccharidosis I dogs following intrathecal recombinant human iduronidase.Glycosaminoglycan storage disorders: a reviewMorphologic and biochemical studies of canine mucopolysaccharidosis I.Suramin-induced storage disease. Mucopolysaccharidosis.Enzyme replacement in a canine model of Hurler syndrome.Regional assignment of the structural gene for human alpha-L-iduronidaseDiffusion tensor imaging and myelin composition analysis reveal abnormal myelination in corpus callosum of canine mucopolysaccharidosis I.Features of brain MRI in dogs with treated and untreated mucopolysaccharidosis type IInadvertent propagation of factor VII deficiency in a canine mucopolysaccharidosis type I research breeding colony.Characterization of an MPS I-H knock-in mouse that carries a nonsense mutation analogous to the human IDUA-W402X mutation.A canine model of human alpha-L-iduronidase deficiency.Diffusion tensor imaging findings suggestive of white matter alterations in a canine model of mucopolysaccharidosis type I.Prolonged Expression of Secreted Enzymes in Dogs After Liver-Directed Delivery of Sleeping Beauty Transposons: Implications for Non-Viral Gene Therapy of Systemic Disease.Substrate Deprivation Therapy to Reduce Glycosaminoglycan Synthesis Improves Aspects of Neurological and Skeletal Pathology in MPS I Mice.
P2860
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P2860
Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I.
description
1982 nî lūn-bûn
@nan
1982年の論文
@ja
1982年論文
@yue
1982年論文
@zh-hant
1982年論文
@zh-hk
1982年論文
@zh-mo
1982年論文
@zh-tw
1982年论文
@wuu
1982年论文
@zh
1982年论文
@zh-cn
name
Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I.
@ast
Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I.
@en
type
label
Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I.
@ast
Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I.
@en
prefLabel
Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I.
@ast
Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I.
@en
P2093
P2860
P1476
Canine alpha-L-iduronidase deficiency. A model of mucopolysaccharidosis I
@en
P2093
E F Neufeld
E Spellacy
G Constantopoulos
R J Munger
P2860
P304
P407
P577
1982-11-01T00:00:00Z