Enzyme replacement in a canine model of Hurler syndrome. - Wikidata - wikimedia - TriplyDB

Enzyme replacement in a canine model of Hurler syndrome.

Enzyme replacement in a canine model of Hurler syndrome.

http://www.wikidata.org/entity/Q36013555

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Recombinant human acid alpha-glucosidase corrects acid alpha-glucosidase-deficient human fibroblasts, quail fibroblasts, and quail myoblasts Newborn screening and diagnosis of mucopolysaccharidoses Pentosan Polysulfate: Oral Versus Subcutaneous Injection in Mucopolysaccharidosis Type I Dogs Therapeutic neonatal hepatic gene therapy in mucopolysaccharidosis VII dogs.Decreased performance in IDUA knockout mouse mimic limitations of joint function and locomotion in patients with Hurler syndrome Evaluation of accumulated mucopolysaccharides in the brain of patients with mucopolysaccharidoses by (1)H-magnetic resonance spectroscopy before and after bone marrow transplantation.Radiographic evaluation of bones and joints in mucopolysaccharidosis I and VII dogs after neonatal gene therapy.Enhancement of drug delivery: enzyme-replacement therapy for murine Morquio A syndrome.Laronidase replacement therapy and left ventricular function in mucopolysaccharidosis I.Enzyme replacement therapy for the mucopolysaccharide storage disorders.Arterial pathology in canine mucopolysaccharidosis-I and response to therapy Biodistribution and pharmacodynamics of recombinant human alpha-L-iduronidase (rhIDU) in mucopolysaccharidosis type I-affected cats following multiple intrathecal administrations Glycosaminoglycan storage disorders: a review Successful induction of immune tolerance to enzyme replacement therapy in canine mucopolysaccharidosis I Electrocardiographic and other cardiac anomalies in beta-glucuronidase-null mice corrected by nonablative neonatal marrow transplantation Hematopoietic stem cell transplantation improves the high incidence of neutralizing allo-antibodies observed in Hurler's syndrome after pharmacological enzyme replacement therapy.IgG-enzyme fusion protein: pharmacokinetics and anti-drug antibody response in rhesus monkeys.Immune tolerance improves the efficacy of enzyme replacement therapy in canine mucopolysaccharidosis I.Carbohydrate structures of recombinant human alpha-L-iduronidase secreted by Chinese hamster ovary cells.Enhancement of drug delivery to bone: characterization of human tissue-nonspecific alkaline phosphatase tagged with an acidic oligopeptide.Bone marrow transplantation for feline mucopolysaccharidosis I.Enzyme replacement therapy in a feline model of Maroteaux-Lamy syndrome.Enzyme replacement therapy from birth in a feline model of mucopolysaccharidosis type VI.Murine mucopolysaccharidosis type VII: long term therapeutic effects of enzyme replacement and enzyme replacement followed by bone marrow transplantation.Enzyme replacement therapy for murine mucopolysaccharidosis type VII leads to improvements in behavior and auditory function.Long-term in vitro correction of alpha-L-iduronidase deficiency (Hurler syndrome) in human bone marrow.Cell microencapsulation: a potential tool for the treatment of neuronopathic lysosomal storage diseases.Lipoprotein receptor binding, cellular uptake, and lysosomal delivery of fusions between the receptor-associated protein (RAP) and alpha-L-iduronidase or acid alpha-glucosidase.Enzyme replacement therapy in Hurler syndrome after failure of hematopoietic transplant.Lysosomal enzyme replacement therapies: Historical development, clinical outcomes, and future perspectives.Elevated cerebral spinal fluid biomarkers in children with mucopolysaccharidosis I-H High-dose enzyme replacement therapy in murine Hurler syndrome alpha-L-iduronidase therapy for mucopolysaccharidosis type I.Neonatal tolerance induction enables accurate evaluation of gene therapy for MPS I in a canine model.Immune response hinders therapy for lysosomal storage diseases.Randomized controlled trial of Hepatitis B virus vaccine in HIV-1-infected patients comparing two different doses.Expression, purification and characterization of recombinant caprine N-acetylglucosamine-6-sulphatase.Joint and bone disease in mucopolysaccharidoses VI and VII: identification of new therapeutic targets and biomarkers using animal models.Haematopoietic cell transplantation (HCT) in combination with enzyme replacement therapy (ERT) in patients with Hurler syndrome.Safety and efficacy of enzyme replacement therapy in combination with hematopoietic stem cell transplantation in Hurler syndrome.

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P2860

Enzyme replacement in a canine model of Hurler syndrome.

http://www.wikidata.org/entity/Q36013555

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1994 nî lūn-bûn

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1994年学术文章

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1994年学术文章

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1994年学术文章

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1994年学术文章

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1994年學術文章

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1994年學術文章

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1994年學術文章

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Enzyme replacement in a canine model of Hurler syndrome.

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Enzyme replacement in a canine model of Hurler syndrome.

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Enzyme replacement in a canine model of Hurler syndrome.

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Enzyme replacement in a canine model of Hurler syndrome.

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Enzyme replacement in a canine model of Hurler syndrome.

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PNAS.91.26.12937

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Proceedings of the National Academy of Sciences of the United States of America

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Enzyme replacement in a canine model of Hurler syndrome.

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P2093

A J Jonas

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E D Kakkis

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E F Neufeld

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M F McEntee

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R M Shull

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S A Kania

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P2860

A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

Identification of mutations in the alpha-L-iduronidase gene (IDUA) that cause Hurler and Scheie syndromes

Enzyme therapy in Gaucher disease type 1: dosage efficacy and adverse effects in 33 patients treated for 6 to 24 months.

Enzyme replacement therapy for murine mucopolysaccharidosis type VII

Bone marrow transplantation in canine mucopolysaccharidosis I. Effects within the central nervous system.

Long-term effects of bone marrow transplantation in dogs with mucopolysaccharidosis I.

The defect in the Hurler and Scheie syndromes: deficiency of -L-iduronidase

Phosphohexosyl components of a lysosomal enzyme are recognized by pinocytosis receptors on human fibroblasts.

Bone marrow transplantation corrects the enzyme defect in neurons of the central nervous system in a lysosomal storage disease

Molecular analysis of Hurler syndrome in Druze and Muslim Arab patients in Israel: multiple allelic mutations of the IDUA gene in a small geographic area.

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12937-12941

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