Primary hemophagocytic syndromes point to a direct link between lymphocyte cytotoxicity and homeostasis.
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Munc18-2 deficiency causes familial hemophagocytic lymphohistiocytosis type 5 and impairs cytotoxic granule exocytosis in patient NK cellsFamilial hemophagocytic lymphohistiocytosis type 5 (FHL-5) is caused by mutations in Munc18-2 and impaired binding to syntaxin 11Macrophage activation syndrome in patients with systemic juvenile idiopathic arthritis is associated with MUNC13-4 polymorphismsDefective cytotoxic lymphocyte degranulation in syntaxin-11 deficient familial hemophagocytic lymphohistiocytosis 4 (FHL4) patientsHemophagocytic Lymphohistiocytosis in Children: Pathogenesis and TreatmentInfectious MononucleosisThe role of CD8 T lymphocytes in rickettsial infectionsHemophagocytic lymphohistiocytosis: an update on diagnosis and pathogenesisRab27a controls HIV-1 assembly by regulating plasma membrane levels of phosphatidylinositol 4,5-bisphosphateInfectious mononucleosis.Macrophage activation syndrome: advances towards understanding pathogenesisProtein kinase Cdelta regulates antigen receptor-induced lytic granule polarization in mouse CD8+ CTLEBAG9 tempers lymphocyte killing activity.Herpes-virus infection in patients with Langerhans cell histiocytosis: a case-controlled sero-epidemiological study, and in situ analysis.Genotype-phenotype study of familial haemophagocytic lymphohistiocytosis type 3A case report of novel mutation in PRF1 gene, which causes familial autosomal recessive hemophagocytic lymphohistiocytosis.Immunopathogenesis of coronavirus infections: implications for SARS.Perforin-mediated target-cell death and immune homeostasis.Death by a thousand cuts: granzyme pathways of programmed cell deathPrimary immunodeficiencies: a field in its infancy.Epstein-Barr virus-positive T/NK-cell lymphoproliferative disordersWhole-exome sequencing reveals overlap between macrophage activation syndrome in systemic juvenile idiopathic arthritis and familial hemophagocytic lymphohistiocytosisPerforin is a critical physiologic regulator of T-cell activation.The biological basis of severe outcomes in Anaplasma phagocytophilum infection.Diffuse large B-cell lymphoma in an adolescent female presenting with Epstein-Barr virus-driven hemophagocytic lymphohistiocytosis: a case report.Haemopoietic stem cell transplantation for genetic disorders.Reactive hemophagocytic syndrome complicating the treatment of inflammatory bowel disease.Detection of Epstein-Barr Virus DNA in Langerhans Cell HistiocytosisImmunity to microbes: lessons from primary immunodeficiencies.Epitope specificity of memory CD8+ T cells dictates vaccination-induced mortality in LCMV-infected perforin-deficient miceCytomegalovirus and Langerhans Cell Histiocytosis: Is There a Link?Inflammation on the mind: visualizing immunity in the central nervous system.Griscelli syndrome-type 2 in twin siblings: case report and update on RAB27A human mutations and gene structure.Graded defects in cytotoxicity determine severity of hemophagocytic lymphohistiocytosis in humans and miceInherited defects in lymphocyte cytotoxic activity.Familial haemophagocytic lymphohistiocytosis: advances in the genetic basis, diagnosis and management.Familial hemophagocytic lymphohistiocytosis: a model for understanding the human machinery of cellular cytotoxicity.Macrophage activation syndrome as part of systemic juvenile idiopathic arthritis: diagnosis, genetics, pathophysiology and treatment.Hereditary and acquired hemophagocytic lymphohistiocytosis.Advances in immunopathogenesis of macrophage activation syndrome during rheumatic inflammatory diseases: toward new therapeutic targets?
P2860
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P2860
Primary hemophagocytic syndromes point to a direct link between lymphocyte cytotoxicity and homeostasis.
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年学术文章
@wuu
2005年学术文章
@zh-cn
2005年学术文章
@zh-hans
2005年学术文章
@zh-my
2005年学术文章
@zh-sg
2005年學術文章
@yue
2005年學術文章
@zh
2005年學術文章
@zh-hant
name
Primary hemophagocytic syndrom ...... cytotoxicity and homeostasis.
@ast
Primary hemophagocytic syndrom ...... cytotoxicity and homeostasis.
@en
type
label
Primary hemophagocytic syndrom ...... cytotoxicity and homeostasis.
@ast
Primary hemophagocytic syndrom ...... cytotoxicity and homeostasis.
@en
prefLabel
Primary hemophagocytic syndrom ...... cytotoxicity and homeostasis.
@ast
Primary hemophagocytic syndrom ...... cytotoxicity and homeostasis.
@en
P2860
P50
P1476
Primary hemophagocytic syndrom ...... cytotoxicity and homeostasis.
@en
P2093
Jérôme Feldmann
P2860
P304
P356
10.1111/J.0105-2896.2005.00224.X
P577
2005-02-01T00:00:00Z