What's new in cystic fibrosis? From treating symptoms to correction of the basic defect.
about
Ion transporting proteins of human bronchial epitheliumDisease-specific clinical trials networks: the example of cystic fibrosisStructural and biophysical properties of a synthetic channel-forming peptide: designing a clinically relevant anion selective pore.Cross-sectional and longitudinal comparisons of the predominant fecal microbiota compositions of a group of pediatric patients with cystic fibrosis and their healthy siblings.Cystic fibrosis transmembrane conductance regulator (CFTR) potentiator VX-770 (ivacaftor) opens the defective channel gate of mutant CFTR in a phosphorylation-dependent but ATP-independent manner.Emergent properties of proteostasis in managing cystic fibrosis.Salmeterol restores secretory functions in cystic fibrosis airway submucosal gland serous cells.Local modulation of cystic fibrosis conductance regulator: cytoskeleton and compartmentalized cAMP signalling.Airway surface liquid depth measured in ex vivo fragments of pig and human trachea: dependence on Na+ and Cl- channel function.Challenges and advances in the development of inhalable drug formulations for cystic fibrosis lung disease.Searching for a cure for cystic fibrosis. A 25-year quest in a nutshell.Pharmacogenetics of cystic fibrosis treatment.Role of anion exchangers in Cl- and HCO3- secretion by the human airway epithelial cell line Calu-3.Functional stability of rescued delta F508 cystic fibrosis transmembrane conductance regulator in airway epithelial cells.Cystic fibrosis in a Hispanic adolescent.Abnormal CFTR Affects Glucagon Production by Islet α Cells in Cystic Fibrosis and Polycystic Ovarian Syndrome.Search and rescue: finding ways to correct deltaF508 CFTR.Development of primary human nasal epithelial cell cultures for the study of cystic fibrosis pathophysiologyTreating cystic fibrosis infection, inflammation and ion channels
P2860
Q28249772-32F5D71C-BFA0-4183-ACB6-AFEB1C847D4DQ28602703-8634ED03-FD5C-4190-B2BC-C2847EC58BF0Q33991078-DC8CF1F9-DC68-42D3-AA53-964F1AA56F5EQ34021561-A2A9DEC6-C29E-486D-8F64-B751FED39F2AQ34033437-3BB5A756-F7F2-46C8-8B7C-109E84AE30D6Q34576386-B979B5CC-FA6D-4DA5-87C2-32CCC1FA6708Q36568698-E8EB542D-56C8-4895-A174-CD3E5E8B9196Q36783966-169A8FC6-9ED1-4156-AC37-D16DF7185D89Q37475006-AE42CF8A-AC49-4E9D-8950-9A1D87B6B609Q37849777-039590F9-1B00-407B-A239-8CC45CEB76A6Q38633196-699BBFA4-E36D-4AFE-932A-A12BFF339191Q38918082-55D28F11-0D77-443A-A0B9-E0E1CBCA4DC3Q38988279-EDC4430B-9ABA-4AD5-AB55-3DC771E5FA69Q39342530-B3BAACC5-79F7-4659-94D8-641A56D33D04Q40543794-EFD53DAA-92A3-42DD-A558-DF7CCA3C9B01Q45253869-B0664122-C0C7-43EB-8CC0-224BAE22540AQ46085118-A4EEEA0D-39C3-48F7-B06D-16C1A0AFC621Q57913593-C282A102-3CFF-4344-B176-3AA46EFD57ADQ57913625-29DE7C86-8126-45DA-B7AD-836D84052C55
P2860
What's new in cystic fibrosis? From treating symptoms to correction of the basic defect.
description
article científic
@ca
article scientifique
@fr
articolo scientifico
@it
artigo científico
@pt
bilimsel makale
@tr
scientific article published on 04 April 2008
@en
vedecký článok
@sk
vetenskaplig artikel
@sv
videnskabelig artikel
@da
vědecký článek
@cs
name
What's new in cystic fibrosis? From treating symptoms to correction of the basic defect.
@en
What's new in cystic fibrosis? From treating symptoms to correction of the basic defect.
@nl
type
label
What's new in cystic fibrosis? From treating symptoms to correction of the basic defect.
@en
What's new in cystic fibrosis? From treating symptoms to correction of the basic defect.
@nl
prefLabel
What's new in cystic fibrosis? From treating symptoms to correction of the basic defect.
@en
What's new in cystic fibrosis? From treating symptoms to correction of the basic defect.
@nl
P2093
P2860
P1476
What's new in cystic fibrosis? From treating symptoms to correction of the basic defect.
@en
P2093
François Vermeulen
Kris De Boeck
Marijke Proesmans
P2860
P2888
P304
P356
10.1007/S00431-008-0693-2
P577
2008-04-04T00:00:00Z