An hereditary motor neurone disease with progressive denervation of muscle in the mouse: the mutant 'wobbler'.
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Comparative transcription map of the wobbler critical region on mouse chromosome 11 and the homologous region on human chromosome 2p13-14.VPS54 and the wobbler mouseEdaravone, a Free Radical Scavenger, Delayed Symptomatic and Pathological Progression of Motor Neuron Disease in the Wobbler MouseAutosomal dominance in a late-onset motor neuron disease in the mouseChronic proximal spinal muscular atrophy of childhood and adolescence: sex influenceAnimal models of tremor.Intricate effects of primary motor neuronopathy on contractile proteins and metabolic muscle enzymes as revealed by label-free mass spectrometry.The structure and composition of peripheral nerves and nerve roots in the Sprawling mouse.Longitudinal tracking of human fetal cells labeled with super paramagnetic iron oxide nanoparticles in the brain of mice with motor neuron diseasePathoproteomics of testicular tissue deficient in the GARP component VPS54: the wobbler mouse model of globozoospermia.Mutation of Vps54 causes motor neuron disease and defective spermiogenesis in the wobbler mouse.Genetic rodent models of amyotrophic lateral sclerosisThe nosology of the spinal muscular atrophies.Transport according to GARP: receiving retrograde cargo at the trans-Golgi network.The Wobbler mouse model of amyotrophic lateral sclerosis (ALS) displays hippocampal hyperexcitability, and reduced number of interneurons, but no presynaptic vesicle release impairments.Nonhematopoietic erythropoietin derivatives prevent motoneuron degeneration in vitro and in vivo.Failure of acrosome formation and globozoospermia in the wobbler mouse, a Vps54 spontaneous recessive mutant.Inflammation and neuronal death in the motor cortex of the wobbler mouse, an ALS animal model.Animal model of human disease: Werdnig-Hoffmann disease (infantile spinal muscular atrophy).Needs for animal models of human diseases of the nervous system.Studies on a murine form of spontaneous lower motor neuron degeneration--the wobbler (wa) mouse.Synthesis and localization of ciliary neurotrophic factor in the sciatic nerve of the adult rat after lesion and during regenerationThe therapeutic potential of insulin-like growth factor-1 in central nervous system disorders.The wobbler mouse, an ALS animal model.Amyotrophic lateral sclerosis: Protein chaperone dysfunction revealed by proteomic studies of animal modelsCalcium-binding protein, parvalbumin, is reduced in mutant mammalian muscle with abnormal contractile properties.Endocytic membrane trafficking and neurodegenerative disease.Inherited neuromuscular diseases in the mouse. A review of the literature.Clinical and pathological findings in an unusual infantile motor neurone disease.Spinal motor neurones in murine muscular dystrophy and spinal muscular atrophy. A quantitative histological study.Emetine myopathy in the rat.Specific isomyosin proportions in hyperexcitable and physiologically denervated mouse muscle.Elevated expression of membrane type 1 metalloproteinase (MT1-MMP) in reactive astrocytes following neurodegeneration in mouse central nervous system.Host genetic background influences diverse neurological responses to viral infection in mice.Role of brain-derived neurotrophic factor in wobbler mouse motor neuron disease.Evaluation of the Golgi trafficking protein VPS54 (wobbler) as a candidate for ALS.Reduced GABAergic inhibition explains cortical hyperexcitability in the wobbler mouse model of ALS.Male-sterile phenotype of the neurological mouse mutant weaver.Comparison of pre- and post-implantation development following the application of three artificial activating stimuli in a mouse model with round-headed sperm cells deficient for oocyte activation.Spinal muscular atrophy gene wobbler of the mouse: evidence from chimeric spinal cord and testis for cell-autonomous function.
P2860
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P2860
An hereditary motor neurone disease with progressive denervation of muscle in the mouse: the mutant 'wobbler'.
description
article científic
@ca
article scientifique
@fr
articolo scientifico
@it
artigo científico
@pt
bilimsel makale
@tr
scientific article published on December 1968
@en
vedecký článok
@sk
vetenskaplig artikel
@sv
videnskabelig artikel
@da
vědecký článek
@cs
name
An hereditary motor neurone di ...... e mouse: the mutant 'wobbler'.
@en
An hereditary motor neurone di ...... e mouse: the mutant 'wobbler'.
@nl
type
label
An hereditary motor neurone di ...... e mouse: the mutant 'wobbler'.
@en
An hereditary motor neurone di ...... e mouse: the mutant 'wobbler'.
@nl
prefLabel
An hereditary motor neurone di ...... e mouse: the mutant 'wobbler'.
@en
An hereditary motor neurone di ...... e mouse: the mutant 'wobbler'.
@nl
P2860
P356
P1476
An hereditary motor neurone di ...... e mouse: the mutant 'wobbler'.
@en
P2093
P2860
P304
P356
10.1136/JNNP.31.6.535
P407
P577
1968-12-01T00:00:00Z