Activation of the transcription factor EB rescues lysosomal abnormalities in cystinotic kidney cells.
about
TFEB at a glanceCystinosis (ctns) zebrafish mutant shows pronephric glomerular and tubular dysfunction.The renal Fanconi syndrome in cystinosis: pathogenic insights and therapeutic perspectives.Small molecules as therapeutic agents for inborn errors of metabolism.Autophagy modulation: a potential therapeutic approach in cardiac hypertrophy.Cystinosin, the small GTPase Rab11, and the Rab7 effector RILP regulate intracellular trafficking of the chaperone-mediated autophagy receptor LAMP2A.Effects of long-term cysteamine treatment in patients with cystinosis.Impaired autophagy bridges lysosomal storage disease and epithelial dysfunction in the kidney.HDAC6 Inhibition Promotes Transcription Factor EB Activation and Is Protective in Experimental Kidney Disease.Nephropathic Cystinosis: Symptoms, Treatment, and Perspectives of a Systemic Disease.First Successful Conception Induced by a Male Cystinosis Patient.Advanced glycation end-products suppress autophagic flux in podocytes by activating mammalian target of rapamycin and inhibiting nuclear translocation of transcription factor EB.mTOR-dependent phosphorylation controls TFEB nuclear export
P2860
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P2860
Activation of the transcription factor EB rescues lysosomal abnormalities in cystinotic kidney cells.
description
2016 nî lūn-bûn
@nan
2016年の論文
@ja
2016年論文
@yue
2016年論文
@zh-hant
2016年論文
@zh-hk
2016年論文
@zh-mo
2016年論文
@zh-tw
2016年论文
@wuu
2016年论文
@zh
2016年论文
@zh-cn
name
Activation of the transcriptio ...... es in cystinotic kidney cells.
@en
type
label
Activation of the transcriptio ...... es in cystinotic kidney cells.
@en
prefLabel
Activation of the transcriptio ...... es in cystinotic kidney cells.
@en
P2093
P50
P1433
P1476
Activation of the transcriptio ...... es in cystinotic kidney cells.
@en
P2093
Andrea Ballabio
Anna Taranta
Elena Polishchuk
Francesco Bellomo
Francesco Emma
Laura R Rega
Roman Polishchuk
Sandro Montefusco
P304
P356
10.1016/J.KINT.2015.12.045
P407
P50
P577
2016-04-01T00:00:00Z