Lipid hydroperoxide formation in the retina: correlation with retinal degeneration and light damage in a rat model of Smith-Lemli-Opitz syndrome.
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An oxysterol biomarker for 7-dehydrocholesterol oxidation in cell/mouse models for Smith-Lemli-Opitz syndromeLipid biomarkers of oxidative stress in a genetic mouse model of Smith-Lemli-Opitz syndrome7-Dehydrocholesterol-derived oxysterols and retinal degeneration in a rat model of Smith-Lemli-Opitz syndromeHaploinsufficiency of RanBP2 is neuroprotective against light-elicited and age-dependent degeneration of photoreceptor neuronsQuantitative proteomics analysis of inborn errors of cholesterol synthesis: identification of altered metabolic pathways in DHCR7 and SC5D deficiencyOxysterols from free radical chain oxidation of 7-dehydrocholesterol: product and mechanistic studies.Light-induced exacerbation of retinal degeneration in a rat model of Smith-Lemli-Opitz syndrome.Cone ERG responses in patients with Smith-Lemli-Opitz Syndrome (SLOS).Biological activities of 7-dehydrocholesterol-derived oxysterols: implications for Smith-Lemli-Opitz syndromeAntioxidant supplementation ameliorates molecular deficits in Smith-Lemli-Opitz syndromeMalformation syndromes caused by disorders of cholesterol synthesis.Probing lipid-protein adduction with alkynyl surrogates: application to Smith-Lemli-Opitz syndrome.Novel oxysterols observed in tissues and fluids of AY9944-treated rats: a model for Smith-Lemli-Opitz syndrome.Free radical oxidation of cholesterol and its precursors: Implications in cholesterol biosynthesis disorders.Partial rescue of retinal function and sterol steady-state in a rat model of Smith-Lemli-Opitz syndrome.Assays of plasma dehydrocholesteryl esters and oxysterols from Smith-Lemli-Opitz syndrome patientsRate constants for peroxidation of polyunsaturated fatty acids and sterols in solution and in liposomes.A perspective on free radical autoxidation: the physical organic chemistry of polyunsaturated fatty acid and sterol peroxidation.A highly sensitive method for analysis of 7-dehydrocholesterol for the study of Smith-Lemli-Opitz syndromePhotodamage generates 7-keto- and 7-hydroxycholesterol in the rat retina via a free radical-mediated mechanism.Retinal light damage: mechanisms and protection.Probes for protein adduction in cholesterol biosynthesis disorders: Alkynyl lanosterol as a viable sterol precursor.Retinal degeneration in a rat model of Smith-Lemli-Opitz Syndrome: thinking beyond cholesterol deficiency.Neurotrophin family members as neuroprotectants in retinal degenerations.Light-induced photoreceptor and RPE degeneration involve zinc toxicity and are attenuated by pyruvate, nicotinamide, or cyclic light.Hypothesis: the role of sterols in autism spectrum disorder.Antioxidants: The Missing Key to Improved Therapeutic Intervention in Smith-Lemli-Opitz Syndrome?A reduced zinc diet or zinc transporter 3 knockout attenuate light induced zinc accumulation and retinal degeneration.MiR-211 is essential for adult cone photoreceptor maintenance and visual function.Prevention of Retinal Degeneration in a Rat Model of Smith-Lemli-Opitz Syndrome.Propagation rate constants for the peroxidation of sterols on the biosynthetic pathway to cholesterol.Protective Effect of Highly Polymeric A-Type Proanthocyanidins from Seed Shells of Japanese Horse Chestnut (Aesculus turbinata BLUME) against Light-Induced Oxidative Damage in Rat Retina.Oxysterols and Retinal Degeneration in a Rat Model of Smith-Lemli-Opitz Syndrome: Implications for an Improved Therapeutic Intervention
P2860
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P2860
Lipid hydroperoxide formation in the retina: correlation with retinal degeneration and light damage in a rat model of Smith-Lemli-Opitz syndrome.
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年論文
@yue
2005年論文
@zh-hant
2005年論文
@zh-hk
2005年論文
@zh-mo
2005年論文
@zh-tw
2005年论文
@wuu
2005年论文
@zh
2005年论文
@zh-cn
name
Lipid hydroperoxide formation ...... of Smith-Lemli-Opitz syndrome.
@en
Lipid hydroperoxide formation ...... of Smith-Lemli-Opitz syndrome.
@nl
type
label
Lipid hydroperoxide formation ...... of Smith-Lemli-Opitz syndrome.
@en
Lipid hydroperoxide formation ...... of Smith-Lemli-Opitz syndrome.
@nl
prefLabel
Lipid hydroperoxide formation ...... of Smith-Lemli-Opitz syndrome.
@en
Lipid hydroperoxide formation ...... of Smith-Lemli-Opitz syndrome.
@nl
P2093
P2860
P1476
Lipid hydroperoxide formation ...... of Smith-Lemli-Opitz syndrome.
@en
P2093
Barbara A Nagel
Michael J Richards
Steven J Fliesler
P2860
P304
P356
10.1016/J.EXER.2005.08.016
P577
2005-09-30T00:00:00Z